Behavioral characterization of mouse models of neuroferritinopathy.
Ferritin is the main intracellular protein of iron storage with a central role in the regulation of iron metabolism and detoxification. Nucleotide insertions in the last exon of the ferritin light chain cause a neurodegenerative disease known as Neuroferritinopathy, characterized by iron deposition...
Main Authors: | Sara Capoccia, Federica Maccarinelli, Barbara Buffoli, Luigi F Rodella, Ottavio Cremona, Paolo Arosio, Francesca Cirulli |
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Format: | Article |
Language: | English |
Published: |
Public Library of Science (PLoS)
2015-01-01
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Series: | PLoS ONE |
Online Access: | http://europepmc.org/articles/PMC4331086?pdf=render |
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