Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy
The paper gives 2 clinical examples of patients with the same diagnosis of progressive X-linked Emery-Dreifuss muscular dystrophy and the different course of rhythm and conduction disorders, which have determined various approaches to management tactics. There is evidence for a differential approach...
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Ltd. “The National Academy of Pediatric Science and Innovation”
2016-03-01
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| Series: | Rossijskij Vestnik Perinatologii i Pediatrii |
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| Online Access: | https://www.ped-perinatology.ru/jour/article/view/137 |
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doaj-c077b41a394f43b1b0c362801ceb125b2021-07-28T16:27:43ZrusLtd. “The National Academy of Pediatric Science and Innovation”Rossijskij Vestnik Perinatologii i Pediatrii1027-40652500-22282016-03-016046368130Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathyO. S. Groznova0G. E. Rudenskaya1T. A. Adyan2D. A. Kharlamov3Research Clinical Institute of Pediatrics, N.I. Pirogov Russian National Research Medical University, Moscow; Research Center for Medical Genetics, Russian Academy of Medical Sciences, MoscowResearch Clinical Institute of Pediatrics, N.I. Pirogov Russian National Research Medical University, Moscow; Research Center for Medical Genetics, Russian Academy of Medical Sciences, MoscowResearch Clinical Institute of Pediatrics, N.I. Pirogov Russian National Research Medical University, Moscow; Research Center for Medical Genetics, Russian Academy of Medical Sciences, MoscowResearch Clinical Institute of Pediatrics, N.I. Pirogov Russian National Research Medical University, Moscow; Research Center for Medical Genetics, Russian Academy of Medical Sciences, MoscowThe paper gives 2 clinical examples of patients with the same diagnosis of progressive X-linked Emery-Dreifuss muscular dystrophy and the different course of rhythm and conduction disorders, which have determined various approaches to management tactics. There is evidence for a differential approach to pacemaker implantation, by confirming the correctness of management tactics in a long-term follow-up. A 27-year-old patient had no indications for pacemaker implantation. The other patient aged 13 years was found to have indications and underwent implantation; however, thrombi formed on the electrodes and the atrial electrode needed to be further disconnected.https://www.ped-perinatology.ru/jour/article/view/137childrenprogressive muscular dystrophyemery—dreifuss myopathyx-linked formcardiovascular disorderscardiomy-opathyarrhythmiaspacemaker. |
| collection |
DOAJ |
| language |
Russian |
| format |
Article |
| sources |
DOAJ |
| author |
O. S. Groznova G. E. Rudenskaya T. A. Adyan D. A. Kharlamov |
| spellingShingle |
O. S. Groznova G. E. Rudenskaya T. A. Adyan D. A. Kharlamov Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy Rossijskij Vestnik Perinatologii i Pediatrii children progressive muscular dystrophy emery—dreifuss myopathy x-linked form cardiovascular disorders cardiomy-opathy arrhythmias pacemaker. |
| author_facet |
O. S. Groznova G. E. Rudenskaya T. A. Adyan D. A. Kharlamov |
| author_sort |
O. S. Groznova |
| title |
Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy |
| title_short |
Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy |
| title_full |
Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy |
| title_fullStr |
Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy |
| title_full_unstemmed |
Differential approach to treating life-threatening arrhythmogenic conditions in patients with X-linked Emery—Dreifuss myopathy |
| title_sort |
differential approach to treating life-threatening arrhythmogenic conditions in patients with x-linked emery—dreifuss myopathy |
| publisher |
Ltd. “The National Academy of Pediatric Science and Innovation” |
| series |
Rossijskij Vestnik Perinatologii i Pediatrii |
| issn |
1027-4065 2500-2228 |
| publishDate |
2016-03-01 |
| description |
The paper gives 2 clinical examples of patients with the same diagnosis of progressive X-linked Emery-Dreifuss muscular dystrophy and the different course of rhythm and conduction disorders, which have determined various approaches to management tactics. There is evidence for a differential approach to pacemaker implantation, by confirming the correctness of management tactics in a long-term follow-up. A 27-year-old patient had no indications for pacemaker implantation. The other patient aged 13 years was found to have indications and underwent implantation; however, thrombi formed on the electrodes and the atrial electrode needed to be further disconnected. |
| topic |
children progressive muscular dystrophy emery—dreifuss myopathy x-linked form cardiovascular disorders cardiomy-opathy arrhythmias pacemaker. |
| url |
https://www.ped-perinatology.ru/jour/article/view/137 |
| work_keys_str_mv |
AT osgroznova differentialapproachtotreatinglifethreateningarrhythmogenicconditionsinpatientswithxlinkedemerydreifussmyopathy AT gerudenskaya differentialapproachtotreatinglifethreateningarrhythmogenicconditionsinpatientswithxlinkedemerydreifussmyopathy AT taadyan differentialapproachtotreatinglifethreateningarrhythmogenicconditionsinpatientswithxlinkedemerydreifussmyopathy AT dakharlamov differentialapproachtotreatinglifethreateningarrhythmogenicconditionsinpatientswithxlinkedemerydreifussmyopathy |
| _version_ |
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