Cystic partially differentiated nephroblastoma: a rare pediatric renal tumor—case report

• Main Authors: Leonardo Passos Vilares Cordeiro, Ana Cristina Macedo Carvalho, Isabela Maria Silva, Fabiana Paiva Martins, Aline Pimentel Amaro, Eduardo Miranda Carvalho
• Format: Article
• Language: English
• Published: Elsevier 2020-08-01
• Series: Radiology Case Reports
• Subjects: Cystic partially differentiated nephroblastoma; Multicystic renal tumors; Cystic nephroma; Cystic Wilms’ tumor; Pediatric renal tumors; Magnetic resonance imaging
• Online Access: http://www.sciencedirect.com/science/article/pii/S1930043320301710

Cystic partially differentiated nephroblastoma is a rare renal tumor of childhood. It is part of a spectrum of multicystic renal tumors that also includes cystic nephroma and cystic Wilms’ tumor. We present a case of cystic partially differentiated nephroblastoma, highlighting the clinical and imaging diagnostic challenge. Although the histological diagnostic criteria for all these 3 entities are well established, they are clinically and radiologically indistinguishable. Cystic partially differentiated nephroblastoma is often observed in male children under 2 years old. Typical clinical presentations include abdominal masses, abdominal pain and/or hematuria. Patients should be treated according to tumor histology and stage.