ANGIOSARCOMA OF THE HEART – CLINICAL CASE

• Main Authors: N. Yu. Karpova, M. A. Rashid, T. V. Kazakova, N. S. Chipigina, A. V. Aksenova, R. V. Ershov, Zh. I. Banova, E. M. Levin, A. A. Byshov, B. V. Uvarovskaya
• Format: Article
• Language: English
• Published: Stolichnaya Izdatelskaya Kompaniya 2017-07-01
• Series: Racionalʹnaâ Farmakoterapiâ v Kardiologii
• Subjects: heart tumors; angiosarcoma of the heart; exudative pericarditis; inferior vena cava obstruction; heart failure
• Online Access: https://www.rpcardio.com/jour/article/view/1484
• ISSN: 1819-6446; 2225-3653

Primary angiosarcoma of the heart, constituting 33% of primary heart malignancies in adults, refers to rare diseases with a difficult diagnosis. The article describes the case of primary angiosarcoma of the right atrium, diagnosed posthumously in a patient of 45 years old. The disease debuted in a previously healthy woman 45 years, 2 months before her death. There were episodes of sudden decrease in blood pressure with pain in the chest and short-term loss of consciousness, as well as moderate manifestations of heart failure (hydrothorax, small ascites, hydropericardium, hepatomegaly, leg shunting). The patient died suddenly, a pathologic study revealed an angiosarcoma of the right atrium with invasive growth, accompanied by inferior vena cava stenosis. Angiosarcoma of the heart should be included in a differential diagnosis of patient with pericardial effusion of unspecified genesis, syndromes of vena cava obstruction, unexplained right ventricular failure, syncope with a fall in blood pressure, especially in middle-aged patients.