Sedation in a Patient with Prader-Willi Syndrome: A Case Report

• Main Authors: Hayrettin Daşkaya, Ferda Yılmaz İnal, Mehmet Toptaş, Ümmügülsüm Yazıcı
• Format: Article
• Language: English
• Published: Galenos Yayinevi 2014-12-01
• Series: Haseki Tıp Bülteni
• Subjects: outpatient surgery; electromyography; Prader-Willi syndrome; hypotonia
• Online Access: http://www.hasekidergisi.com/article_7532/Sedation-In-A-Patient-With-Prader-willi-Syndrome-A-Case-Report
• ISSN: 1302-0072; 2147-2688

Prader-Willi syndrome (PWS) is a rare disorder characterized by hypotonia, growth retardation, characteristic face shape, hypogonadism, hyperphagia and related morbid obesity. Anesthesia application in these patients has increased risk of peroperative complication due the central hypotonia, abnormal teeth structure, and limited neck mobility. Therefore, clinicians should be prepared for the worst scenario before anesthesia application in patients with PWS during general or out-patient surgery. Here, in this case report, outpatient anesthesia performed in a patient with PWS for diagnostic electromyography is presented with the literature review.