Surgical intervention for Kasaback-Merritt Syndrome: A case report

Surgical intervention for Kasaback-Merritt Syndrome: A case report

Kasabach-Merritt Syndrome (KMS) is an uncommon phenomenon characterized by the presence of a vascular tumor in association with thrombocytopenia, consumption coagulopathy and hemodynamic instability. Typically presents in infancy and involve the skin and deep soft tissues of the arms and legs. Treat...

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Bibliographic Details
Main Authors: Morris Sasson, J. Alford Flippin, Gary Birken, Fuad Alkhoury
Format: Article
Language:English
Published: Elsevier 2015-10-01
Series:Journal of Pediatric Surgery Case Reports
Subjects:
Kasaback-Merritt Syndrome
Kaposiform hemangioendothelioma
Vascular tumor
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576615001153
Description
Summary:Kasabach-Merritt Syndrome (KMS) is an uncommon phenomenon characterized by the presence of a vascular tumor in association with thrombocytopenia, consumption coagulopathy and hemodynamic instability. Typically presents in infancy and involve the skin and deep soft tissues of the arms and legs. Treatment options vary with clinical presentation, and ranges from medical management to immediate surgical intervention. We present an unusual case of a newborn with KMS and fatal hemodynamic collapse imminent, which was successfully treated with surgical resection at our institution.
ISSN:2213-5766

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