Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement

Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement

Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presente...

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Main Authors: Yashwant Agrawal, Sandeep Patri, Jagadeesh K. Kalavakunta
Format: Article
Language:English
Published: Hindawi Limited 2016-01-01
Series:Case Reports in Pulmonology
Online Access:http://dx.doi.org/10.1155/2016/4397641
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spelling doaj-a990119f1ec54de5abe6cac7f1d4d7c02020-11-24T22:40:47ZengHindawi LimitedCase Reports in Pulmonology2090-68462090-68542016-01-01201610.1155/2016/43976414397641Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander PlacementYashwant Agrawal0Sandeep Patri1Jagadeesh K. Kalavakunta2Department of Internal Medicine/Pediatrics and Internal Medicine, Western Michigan University Homer Stryker School of Medicine, Kalamazoo, MI 49048, USADepartment of Internal Medicine/Pediatrics and Internal Medicine, Western Michigan University Homer Stryker School of Medicine, Kalamazoo, MI 49048, USADepartment of Cardiology, Borgess Medical Center/Michigan State University, Kalamazoo, MI 49048, USACongenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presented with increasing stridor over 1 month. Imaging revealed right lung agenesis, complete dextromalposition of heart, and compression of distal trachea. An intrathoracic saline tissue expander was placed which marked improved distal tracheal stenosis. In patients who are symptomatic it becomes imperative to perform surgeries to increase survival as was the case in this patient.http://dx.doi.org/10.1155/2016/4397641
collection DOAJ
language English
format Article
sources DOAJ
author Yashwant Agrawal
Sandeep Patri
Jagadeesh K. Kalavakunta
spellingShingle Yashwant Agrawal
Sandeep Patri
Jagadeesh K. Kalavakunta
Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
Case Reports in Pulmonology
author_facet Yashwant Agrawal
Sandeep Patri
Jagadeesh K. Kalavakunta
author_sort Yashwant Agrawal
title Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_short Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_full Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_fullStr Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_full_unstemmed Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement
title_sort right lung agenesis with tracheal stenosis due to complete tracheal rings and postpneumonectomy like syndrome treated with tissue expander placement
publisher Hindawi Limited
series Case Reports in Pulmonology
issn 2090-6846
2090-6854
publishDate 2016-01-01
description Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presented with increasing stridor over 1 month. Imaging revealed right lung agenesis, complete dextromalposition of heart, and compression of distal trachea. An intrathoracic saline tissue expander was placed which marked improved distal tracheal stenosis. In patients who are symptomatic it becomes imperative to perform surgeries to increase survival as was the case in this patient.
url http://dx.doi.org/10.1155/2016/4397641
work_keys_str_mv AT yashwantagrawal rightlungagenesiswithtrachealstenosisduetocompletetrachealringsandpostpneumonectomylikesyndrometreatedwithtissueexpanderplacement
AT sandeeppatri rightlungagenesiswithtrachealstenosisduetocompletetrachealringsandpostpneumonectomylikesyndrometreatedwithtissueexpanderplacement
AT jagadeeshkkalavakunta rightlungagenesiswithtrachealstenosisduetocompletetrachealringsandpostpneumonectomylikesyndrometreatedwithtissueexpanderplacement
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