A case of Poland Syndrome associated with dextroposition

A case of Poland Syndrome associated with dextroposition

<p>Abstract</p> <p>Classical Poland Syndrome (PS) is characterized by unilateral, partial or complete absence of the sternocostal head of the major pectoral muscle and brachysyndactyly of fingers on the same side.</p> <p>We report the case of a newborn infant with dextr...

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Main Authors: Guerrini Pietro, Marsella Maria, Lacorte Doriana
Format: Article
Language:English
Published: BMC 2010-02-01
Series:Italian Journal of Pediatrics
Online Access:http://www.ijponline.net/content/36/1/21
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spelling doaj-a900d8a7cd9544a9882a4e785906c2eb2020-11-24T23:34:04ZengBMCItalian Journal of Pediatrics1720-84241824-72882010-02-013612110.1186/1824-7288-36-21A case of Poland Syndrome associated with dextropositionGuerrini PietroMarsella MariaLacorte Doriana<p>Abstract</p> <p>Classical Poland Syndrome (PS) is characterized by unilateral, partial or complete absence of the sternocostal head of the major pectoral muscle and brachysyndactyly of fingers on the same side.</p> <p>We report the case of a newborn infant with dextrocardia and PS located on the left side.</p> <p>This association is very rare: to date only 19 cases have been described in scientific literature. In all reported cases, as in the present, the Poland defect involved the left side and was associated to rib defects, whereas most cases of PS are on the right side and few have rib defects. This case supports the view that dextrocardia follows the loss of volume of the left hemithorax caused by Poland sequence and that the combination of PS and dextrocardia is not coincidental.</p> http://www.ijponline.net/content/36/1/21
collection DOAJ
language English
format Article
sources DOAJ
author Guerrini Pietro
Marsella Maria
Lacorte Doriana
spellingShingle Guerrini Pietro
Marsella Maria
Lacorte Doriana
A case of Poland Syndrome associated with dextroposition
Italian Journal of Pediatrics
author_facet Guerrini Pietro
Marsella Maria
Lacorte Doriana
author_sort Guerrini Pietro
title A case of Poland Syndrome associated with dextroposition
title_short A case of Poland Syndrome associated with dextroposition
title_full A case of Poland Syndrome associated with dextroposition
title_fullStr A case of Poland Syndrome associated with dextroposition
title_full_unstemmed A case of Poland Syndrome associated with dextroposition
title_sort case of poland syndrome associated with dextroposition
publisher BMC
series Italian Journal of Pediatrics
issn 1720-8424
1824-7288
publishDate 2010-02-01
description <p>Abstract</p> <p>Classical Poland Syndrome (PS) is characterized by unilateral, partial or complete absence of the sternocostal head of the major pectoral muscle and brachysyndactyly of fingers on the same side.</p> <p>We report the case of a newborn infant with dextrocardia and PS located on the left side.</p> <p>This association is very rare: to date only 19 cases have been described in scientific literature. In all reported cases, as in the present, the Poland defect involved the left side and was associated to rib defects, whereas most cases of PS are on the right side and few have rib defects. This case supports the view that dextrocardia follows the loss of volume of the left hemithorax caused by Poland sequence and that the combination of PS and dextrocardia is not coincidental.</p>
url http://www.ijponline.net/content/36/1/21
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AT marsellamaria acaseofpolandsyndromeassociatedwithdextroposition
AT lacortedoriana acaseofpolandsyndromeassociatedwithdextroposition
AT guerrinipietro caseofpolandsyndromeassociatedwithdextroposition
AT marsellamaria caseofpolandsyndromeassociatedwithdextroposition
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