Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation

Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis asso...

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Main Authors: Mandeep Singh, Sheharyar K. Merwat, Jeffrey H. Fair, Alexander G. Duarte
Format: Article
Language:English
Published: Elsevier 2021-01-01
Series:Respiratory Medicine Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213007121001052
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spelling doaj-a6e9a9cad84249c4a48a4805272afbf82021-07-31T04:39:31ZengElsevierRespiratory Medicine Case Reports2213-00712021-01-0133101443Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantationMandeep Singh0Sheharyar K. Merwat1Jeffrey H. Fair2Alexander G. Duarte3Corresponding author.; Department of Internal Medicine, University of Texas Medical Branch, Galveston, TX, USADepartment of Internal Medicine, University of Texas Medical Branch, Galveston, TX, USADepartment of Internal Medicine, University of Texas Medical Branch, Galveston, TX, USADepartment of Internal Medicine, University of Texas Medical Branch, Galveston, TX, USAShort telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.http://www.sciencedirect.com/science/article/pii/S2213007121001052Short telomere syndromeIdiopathic pulmonary fibrosisInterstitial lung diseaseLiver cirrhosisLiver transplantLung transplant
collection DOAJ
language English
format Article
sources DOAJ
author Mandeep Singh
Sheharyar K. Merwat
Jeffrey H. Fair
Alexander G. Duarte
spellingShingle Mandeep Singh
Sheharyar K. Merwat
Jeffrey H. Fair
Alexander G. Duarte
Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
Respiratory Medicine Case Reports
Short telomere syndrome
Idiopathic pulmonary fibrosis
Interstitial lung disease
Liver cirrhosis
Liver transplant
Lung transplant
author_facet Mandeep Singh
Sheharyar K. Merwat
Jeffrey H. Fair
Alexander G. Duarte
author_sort Mandeep Singh
title Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
title_short Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
title_full Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
title_fullStr Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
title_full_unstemmed Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
title_sort liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation
publisher Elsevier
series Respiratory Medicine Case Reports
issn 2213-0071
publishDate 2021-01-01
description Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.
topic Short telomere syndrome
Idiopathic pulmonary fibrosis
Interstitial lung disease
Liver cirrhosis
Liver transplant
Lung transplant
url http://www.sciencedirect.com/science/article/pii/S2213007121001052
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AT jeffreyhfair livertransplantrecipientwithrespiratoryfailureduetopulmonaryfibrosisrelatedtotelomerediseaserequiringlungtransplantation
AT alexandergduarte livertransplantrecipientwithrespiratoryfailureduetopulmonaryfibrosisrelatedtotelomerediseaserequiringlungtransplantation
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