Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation

Liver transplant recipient with respiratory failure due to pulmonary fibrosis related to telomere disease requiring lung transplantation

Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis asso...

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Bibliographic Details
Main Authors: Mandeep Singh, Sheharyar K. Merwat, Jeffrey H. Fair, Alexander G. Duarte
Format: Article
Language:English
Published: Elsevier 2021-01-01
Series:Respiratory Medicine Case Reports
Subjects:
Short telomere syndrome
Idiopathic pulmonary fibrosis
Interstitial lung disease
Liver cirrhosis
Liver transplant
Lung transplant
Online Access:http://www.sciencedirect.com/science/article/pii/S2213007121001052
Description
Summary:Short telomere syndrome (STS) is characterized as multiorgan dysfunction presenting with unexplained cytopenias, cryptogenic cirrhosis and pulmonary fibrosis. We present a liver transplant recipient that gradually developed hypoxic respiratory failure attributed to idiopathic pulmonary fibrosis associated telomere disease that culminated in a successful single lung transplantation.
ISSN:2213-0071

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