Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient

Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely repor...

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Bibliographic Details
Main Authors: Beatrice Chia-Hui Shih, Jae Hong Lim, Jooncheol Min, Eung Re Kim, Jae Gun Kwak, Woong-Han Kim
Format: Article
Language:English
Published: Korean Society for Thoracic and Cardiovascular Surgery 2019-04-01
Series:Korean Journal of Thoracic and Cardiovascular Surgery
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Summary:Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.
ISSN:2233-601X
2093-6516