Cerebellar Clear Cell Ependymoma in a 10-Year-Old Girl

• Main Authors: Aye Nyein Thinzar, Jisang Park, Ahrim Moon, Sun Chul Hwang, Hyun Sook Hong, A Leum Lee, Kee-Hyun Chang, Hee Kyung Kim, Susie Chin
• Format: Article
• Language: English
• Published: The Korean Society of Radiology 2016-01-01
• Series: 대한영상의학회지
• Subjects: cerebellum; clear cell ependymoma; mr imaging
• Online Access: https://doi.org/10.3348/jksr.2016.74.1.61

Clear cell ependymoma (CCE) is a histological rare variant (1–5%) of ependymoma, which is distinguished from other histological subtypes by the presence of fusiform cells arrayed radially around small blood vessels. These alleged perivascular pseudorosettes are significant characteristic features of ependymomas. About 95% of infratentorial ependymomas are found in the fourth ventricle and the remainder occurs as cerebellopontine angle lesions. In previous reports, the cerebellum is found to be a rare location for ependymoma. In this study we report one case of CCE originating from the cerebellar hemisphere, showing unusual morphology on 3T MRI.