Case report: surgical resection of right ventricular cardiac fibroma in an adult patient

• Main Authors: Hirohisa Ikegami, Anthony Lemaire, Subhashini Gowda, Billie Fyfe, Mahmoud Ali, Mark J. Russo, Leonard Y. Lee
• Format: Article
• Language: English
• Published: BMC 2021-05-01
• Series: Journal of Cardiothoracic Surgery
• Subjects: Cardiac tumors; Cardiac fibroma; Case report; Histology
• Online Access: https://doi.org/10.1186/s13019-021-01514-x

Abstract Background Cardiac fibromas are rare benign cardiac neoplasms, most frequently occurring in the pediatric population; with very rare cases identified in adults. The tumors are comprised of spindled cells with myofibroblastic ultrastructural features embedded in generally collagenous and elastic stroma. The tumors are intramural in the ventricles, most commonly the left ventricle. Clinical symptoms vary by location and size of tumor and some are asymptomatic. Surgical resection is curative, but rare cases require cardiac transplantation. Case presentation We report an asymptomatic, large, right ventricular fibroma in a 64-year-old woman. The patient underwent open incisional tumor biopsy via lower hemi-sternotomy, followed by complete tumor resection via full sternotomy a week later after confirming the tumor is benign. The tumor was resected using cardiopulmonary bypass, and the defect of right ventricular free wall was repaired using a prosthetic double-patch technique. The postoperative course was uneventful. The patient was discharged to home on day 4 post-complete tumor resection. Conclusion This report expands the existing literature for better comprehension and detection of cardiac fibroma patients and also highlights the various imaging modalities, surgical management, and histological analysis.