Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult

Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity,...

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Main Authors: Hong Ju Shin, Jae Seung Shin
Format: Article
Language:English
Published: Korean Society for Thoracic and Cardiovascular Surgery 2020-06-01
Series:Korean Journal of Thoracic and Cardiovascular Surgery
Subjects:
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spelling doaj-a1d5ea58d87541e6bf8676d8056517772020-11-25T02:33:58ZengKorean Society for Thoracic and Cardiovascular SurgeryKorean Journal of Thoracic and Cardiovascular Surgery2233-601X2093-65162020-06-0153314414610.5090/kjtcs.2020.53.3.144Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old AdultHong Ju Shin0https://orcid.org/0000-0002-0731-3523Jae Seung Shin1https://orcid.org/0000-0001-8147-6665Korea University Ansan Hospital, Korea University College of Medicine, AnsanKorea University Ansan Hospital, Korea University College of Medicine, AnsanSupravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.supravalvar aortic stenosisaortic valve
collection DOAJ
language English
format Article
sources DOAJ
author Hong Ju Shin
Jae Seung Shin
spellingShingle Hong Ju Shin
Jae Seung Shin
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
Korean Journal of Thoracic and Cardiovascular Surgery
supravalvar aortic stenosis
aortic valve
author_facet Hong Ju Shin
Jae Seung Shin
author_sort Hong Ju Shin
title Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_short Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_full Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_fullStr Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_full_unstemmed Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
title_sort aortic valve–sparing surgical treatment of supravalvar aortic stenosis in a 65-year-old adult
publisher Korean Society for Thoracic and Cardiovascular Surgery
series Korean Journal of Thoracic and Cardiovascular Surgery
issn 2233-601X
2093-6516
publishDate 2020-06-01
description Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.
topic supravalvar aortic stenosis
aortic valve
work_keys_str_mv AT hongjushin aorticvalvesparingsurgicaltreatmentofsupravalvaraorticstenosisina65yearoldadult
AT jaeseungshin aorticvalvesparingsurgicaltreatmentofsupravalvaraorticstenosisina65yearoldadult
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