Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult
Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity,...
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Korean Society for Thoracic and Cardiovascular Surgery
2020-06-01
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doaj-a1d5ea58d87541e6bf8676d8056517772020-11-25T02:33:58ZengKorean Society for Thoracic and Cardiovascular SurgeryKorean Journal of Thoracic and Cardiovascular Surgery2233-601X2093-65162020-06-0153314414610.5090/kjtcs.2020.53.3.144Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old AdultHong Ju Shin0https://orcid.org/0000-0002-0731-3523Jae Seung Shin1https://orcid.org/0000-0001-8147-6665Korea University Ansan Hospital, Korea University College of Medicine, AnsanKorea University Ansan Hospital, Korea University College of Medicine, AnsanSupravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS.supravalvar aortic stenosisaortic valve |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Hong Ju Shin Jae Seung Shin |
spellingShingle |
Hong Ju Shin Jae Seung Shin Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult Korean Journal of Thoracic and Cardiovascular Surgery supravalvar aortic stenosis aortic valve |
author_facet |
Hong Ju Shin Jae Seung Shin |
author_sort |
Hong Ju Shin |
title |
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult |
title_short |
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult |
title_full |
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult |
title_fullStr |
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult |
title_full_unstemmed |
Aortic Valve–Sparing Surgical Treatment of Supravalvar Aortic Stenosis in a 65-Year-Old Adult |
title_sort |
aortic valve–sparing surgical treatment of supravalvar aortic stenosis in a 65-year-old adult |
publisher |
Korean Society for Thoracic and Cardiovascular Surgery |
series |
Korean Journal of Thoracic and Cardiovascular Surgery |
issn |
2233-601X 2093-6516 |
publishDate |
2020-06-01 |
description |
Supravalvar aortic stenosis (SVAS) is a rare congenital cardiac disease that usually co-occurs with Williams syndrome. In the adult population, a few SVAS cases have been reported in patients affected by homozygous familial hypercholesterolemia. However, because of the rarity of this disease entity, there is no standard surgical treatment for SVAS. Here, we present a case of successful surgical treatment using an autologous excised aortic patch in a 65-year-old patient with SVAS. |
topic |
supravalvar aortic stenosis aortic valve |
work_keys_str_mv |
AT hongjushin aorticvalvesparingsurgicaltreatmentofsupravalvaraorticstenosisina65yearoldadult AT jaeseungshin aorticvalvesparingsurgicaltreatmentofsupravalvaraorticstenosisina65yearoldadult |
_version_ |
1724811144108965888 |