Limited Cutaneous Scleroderma-Related Pulmonary Arterial Hypertension — a Case Report

Limited Cutaneous Scleroderma-Related Pulmonary Arterial Hypertension — a Case Report

Background: Pulmonary hypertension (PH), defined by mean pulmonary arterial pressure (PAPm) ≥25 mm Hg, can lead to increasing pulmonary vascular resistance, which eventually results in right ventricle failure. Scleroderma, as an autoimmune connective tissue disease, is associated with PH as a sub-gr...

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Bibliographic Details
Main Authors: Ţilea Ioan, Bocicor Elena Andreea, Gal Codruţa Maria, Varga Andreea
Format: Article
Language:English
Published: Sciendo 2016-06-01
Series:Journal of Interdisciplinary Medicine
Subjects:
pulmonary hypertension
connective tissue disease
diagnosis
specific therapy
multidisciplinarity
Online Access:https://doi.org/10.1515/jim-2016-0019
Description
Summary:Background: Pulmonary hypertension (PH), defined by mean pulmonary arterial pressure (PAPm) ≥25 mm Hg, can lead to increasing pulmonary vascular resistance, which eventually results in right ventricle failure. Scleroderma, as an autoimmune connective tissue disease, is associated with PH as a sub-group according to the 2015 ESC/ERS PH classification. Pulmonary arterial hypertension (PAH) associated with scleroderma (SSc-PAH) can often result in poor prognosis with increased mortality. Early diagnosis and specific treatment of PH can significantly improve the prognosis of these patients.
ISSN:2501-8132

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