Congenital orbital teratoma

• Main Authors: Shereen Aiyub, WengOnn Chan, John Szetu, Laurence J Sullivan, John Pater, Peter Cooper, Dinesh Selva
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2013-01-01
• Series: Indian Journal of Ophthalmology
• Subjects: Amblyopia; nasolacrimal duct obstruction; probing; Duane syndrome; esotropia; strabismus; Bevacizumab; mitochondrial function; microvascular endothelial cells; neurosensory retinal cells; retinal pigment epithelial cells; tissue culture; Clinical donor tissue grading; death to enucleation time; death to preservation time; eye bank specular microscopy; optimizing donor tissue utilization; DCR; endodiathermy bipolar probe; recanalize; Age-related macular degeneration; carotenoids; cross-sectional studies; lutein; Children; GDx variable corneal compensation; Indian; normal; retinal nerve fiber layer thickness; Biological amniotic membrane; 5-fluorouracil; retina; trabeculectomy; Clinical features; complications; etiology; retinal vasculitis; Thailand; Coloboma of the choroid; coloboma optic disc; indo cyanine green angiography; vascular pattern; Aphakia; inadequate capsular support; pediatric aphakia; secondary intraocular lens implantation; steel suture; trans-scleral fixation; vanadium steel; Drug reaction; drug-induced; ranibizumab; subacute cutaneous lupus erythematosus; Prevalence; rapid; rapid assessment of refractive errors; spectacles use; uncorrected refractive errors; visual impairment; Bitemporal hemianopia; Traumatic chiasmal syndrome; visual field; Phaeohyphomycosis; pigmented fungi; subretinal abscess; subretinal biopsy; Brimonidine; combination; glaucoma; intraocular pressure; timolol; Congenital; dermis fat graft; orbital; teratoma
• Online Access: http://www.ijo.in/article.asp?issn=0301-4738;year=2013;volume=61;issue=12;spage=767;epage=769;aulast=Aiyub

We present a case of mature congenital orbital teratoma managed with lid-sparing exenteration and dermis fat graft. This is a case report on the management of congenital orbital teratoma. A full-term baby was born in Fiji with prolapsed right globe which was surrounded by a nonpulsatile, cystic mass. Clinical and imaging features were consistent with congenital orbital teratoma. Due to limited surgical expertise, the patient was transferred to Adelaide, Australia for further management. The patient underwent a lid-sparing exenteration with frozen section control of the apical margin. A dermis fat graft from the groin was placed beneath the lid skin to provide volume. Histopathology revealed mature tissues from each of the three germ cell layers which confirmed the diagnosis of mature teratoma. We describe the successful use of demis fat graft in socket reconstruction following lid-sparing exenteration for congenital orbital teratoma.