Primary Cardiac Epithelioid Angiosarcoma in a Latin American Patient: Case Report and Literature Review

Cardiac angiosarcoma is a rare and clinically challenging pathology. It is a high-grade primary malignant tumor of the heart tissue that has many variants, of which the epithelioid variant is rarely present in the heart or the great vessels. As with many other cardiac tumors, it is mainly a diagnosi...

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Bibliographic Details
Main Authors: Dan Morgenstern-Kaplan, Carlos Manuel Aboitiz-Rivera, Ruben Blachman-Braun, María Eugenia Vázquez-Manríquez, Benito Sarabia-Ortega, Mario Enrique Baltazares-Lipp
Format: Article
Language:English
Published: Hindawi Limited 2019-01-01
Series:Case Reports in Oncological Medicine
Online Access:http://dx.doi.org/10.1155/2019/2641976
Description
Summary:Cardiac angiosarcoma is a rare and clinically challenging pathology. It is a high-grade primary malignant tumor of the heart tissue that has many variants, of which the epithelioid variant is rarely present in the heart or the great vessels. As with many other cardiac tumors, it is mainly a diagnosis of exclusion and the initial diagnostic test is an echocardiogram followed by a biopsy with immunohistochemistry analysis to ascertain the type of tumor. The differential diagnosis of cardiac tumors is challenging due to the overlapping clinical manifestations with different cardiac tumors and systemic diseases. Cardiac angiosarcomas are often aggressive with a poor prognosis even with treatment. Herein, we present a case of the epithelioid variant of a cardiac angiosarcoma in addition to a thorough review of the recent literature on the clinical manifestation, diagnosis, and treatment of this type of tumors.
ISSN:2090-6706
2090-6714