Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis

Rosai-Dorfman Disease Involving Multiple Organs: An Unusual Case with Poor Prognosis

Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman diseas...

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Bibliographic Details
Main Authors: Fandresena Arilala Sendrasoa, Irina Mamisoa Ranaivo, Onivola Raharolahy, Malalaniaina Andrianarison, Naina Harinjara Razanakoto, Lala Soavina Ramarozatovo, Fahafahantsoa Rapelanoro Rabenja
Format: Article
Language:English
Published: Hindawi Limited 2016-01-01
Series:Case Reports in Medicine
Online Access:http://dx.doi.org/10.1155/2016/3920516
Description
Summary:Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.
ISSN:1687-9627
1687-9635

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