Heterotaxy syndrome with agenesis of dorsal pancreas and diabetes mellitus: case report and review of the literature

Heterotaxy syndrome with agenesis of dorsal pancreas and diabetes mellitus: case report and review of the literature

SUMMARY Heterotaxy syndrome (HS) is a rare congenital condition with multifactorial heritance, characterized by an abnormal arrangement of thoraco-abdominal organs and vessels. Patients present with multiple cardiac, gastrointestinal, hepatosplenic, pancreatic, renal, neurological and skeletal disor...

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Bibliographic Details
Main Authors:	Cínthia Minatel Riguetto, Samantha Pelichek, Arnaldo Moura Neto
Format:	Article
Language:	English
Published:	Brazilian Society of Endocrinology and Metabolism
Series:	Archives of Endocrinology and Metabolism
Online Access:	http://www.scielo.br/scielo.php?script=sci_arttext&pid=S2359-39972019005004102&lng=en&tlng=en

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