PERIBULBAR COMPLEX CHORISTOMA IN ASSOCIATION WITH IPSILATERAL NASAL HYPOPLASIA AND NASOLACRIMAL DUCT OBSTRUCTION

• Main Authors: S. Z. Tabatabaie, M. T. Rajabi, F. Asadi-Amoli, A. Sadeghi-Tari A. Kasai
• Format: Article
• Language: English
• Published: Tehran University of Medical Sciences 2007-05-01
• Series: Acta Medica Iranica
• Subjects: Complex choristoma; nasal hypoplasia; nasolacrimal duct obstruction
• Online Access: http://journals.tums.ac.ir/PdfMed.aspx?pdf_med=/upload_files/pdf/3449.pdf&manuscript_id=3449

Developmental midline perinasal masses in children are rare lesions specifically in association with choristomas. We encountered a 3-year-old boy with epiphora, a striking mass on the nasal bridge and ipsilateral nasal hypoplasia. CT scan imaging showed multiple calcified areas within the tumor in addition to linear defect in frontal bone, hypoplastic left ethmoidal sinus and left nasal cavity, and absence of left nasal concha. The patient had no history of seizure, no neurologic deficit, and ocular developmental exams were normal. After performing excisional biopsy of the tumor, histopathologic analysis revealed complex choristoma composed of cartilage and bone. The most appropriate name for this malformation, which we have not found described in the literature, seems to be, nasal hypoplasia with complex choristoma and nasolacrimal duct obstruction.