Management of Mixed Hemangiolymphangioma with Kasabach-Merritt Syndrome - A Case Report and Review of Literature

• Main Authors: D. Srinivasan, SreeRamulu P. N., Sangamesh, Harish Kumar. G., Prashanth K. Dhannur
• Format: Article
• Language: English
• Published: Krishna Institute of Medical Sciences University 2014-07-01
• Series: Journal of Krishna Institute of Medical Sciences University
• Subjects: Congenital; Haemangiomas; Kasabach- Merritt Syndrome; Vascular mal-formation
• Online Access: http://www.jkimsu.com/jkimsu-vol3no2/JKIMSU,%20Vol.%203,%20No.%202,%20July-Dec%202014%20Page%20126-128.pdf
• ISSN: 2231-4261; 2231-4261

A young boy of 5 years presented with in our OPD with the globular swelling over the dorsum of right hand with clinical features of vascular haemangioma present from birth, gradually growing with the age and attained the size of 6 x 5 cms never had any bleeding diatheses, platelet count was 80,000 / cumm. Before the platelet could dip surgery was contemplated and excision done. Haemangiomas are vascular lesions resulting from abnormal proliferation of blood vessels. They are the most common pediatric neoplasms. Kasabach-Merritt syndrome is a rare type of vascular lesion with peculiar characteristics. The diagnosis is based upon three basic findings; enlarging hemangioma, thrombocytopenia and consumption coagulopathy. The mortality is nearly 30%. Hemangiomas can be associated with genetic disorder thus chromosome tests (to exclude certain genetic syndromes) is advocated.