Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis

Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis

Major Aortopulmonary Collateral Artery (MAPCA) as an isolated congenital anomaly, without evidence of any structural heart disease, is a very rare observation. Previously published reports indicate that symptomatic infants with large isolated MAPCA usually present with congestive heart failure or...

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Main Authors: Brajesh Kumar Kunwar, Snigdha Paddalwar, Mahesh Ghogare
Format: Article
Language:English
Published: JCDR Research and Publications Private Limited 2017-06-01
Series:Journal of Clinical and Diagnostic Research
Subjects:
amplatzer vascular plug
computed tomography angiogram
sildenafil
Online Access:https://jcdr.net/articles/PDF/10094/27645_CE(EK)_F(RK)_PF1(RU_VT_NE)_PFA(PNE).pdf
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spelling doaj-8e953f18aacb402592837da98b5b73f52020-11-25T03:13:31ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2017-06-01116OD18OD2010.7860/JCDR/2017/27645.10094Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging DiagnosisBrajesh Kumar Kunwar0Snigdha Paddalwar1Mahesh Ghogare2Senior Consultant Interventional Cardiologist and Head, Department of Cardiology, Fortis Hiranandani Hospital, Navi Mumbai, Maharashtra, India.Pediatric Cardiac Anaesthetic, Department of Cardiology, Seven Hills Hospital, Mumbai, Maharashtra, India.Consultant Cardiologist, Department of Cardiology, Seven Hills Hospital, Mumbai, Maharashtra, India.Major Aortopulmonary Collateral Artery (MAPCA) as an isolated congenital anomaly, without evidence of any structural heart disease, is a very rare observation. Previously published reports indicate that symptomatic infants with large isolated MAPCA usually present with congestive heart failure or recurrent respiratory tract infections. To the best of our knowledge, the present case of an infant with large isolated MAPCA is a unique case with a diagnostic dilemma due to presentation with severe pulmonary hypertension as a predominant sign. The infant was managed successfully by percutaneous obliteration with amplatzer vascular plugs, along with perioperative and postoperative sildenafil.https://jcdr.net/articles/PDF/10094/27645_CE(EK)_F(RK)_PF1(RU_VT_NE)_PFA(PNE).pdfamplatzer vascular plugcomputed tomography angiogramsildenafil
collection DOAJ
language English
format Article
sources DOAJ
author Brajesh Kumar Kunwar
Snigdha Paddalwar
Mahesh Ghogare
spellingShingle Brajesh Kumar Kunwar
Snigdha Paddalwar
Mahesh Ghogare
Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis
Journal of Clinical and Diagnostic Research
amplatzer vascular plug
computed tomography angiogram
sildenafil
author_facet Brajesh Kumar Kunwar
Snigdha Paddalwar
Mahesh Ghogare
author_sort Brajesh Kumar Kunwar
title Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis
title_short Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis
title_full Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis
title_fullStr Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis
title_full_unstemmed Large Isolated Major Aortopulmonary Collateral Artery Causing Severe Pulmonary Hypertension in an Infant: A Rare and Challenging Diagnosis
title_sort large isolated major aortopulmonary collateral artery causing severe pulmonary hypertension in an infant: a rare and challenging diagnosis
publisher JCDR Research and Publications Private Limited
series Journal of Clinical and Diagnostic Research
issn 2249-782X
0973-709X
publishDate 2017-06-01
description Major Aortopulmonary Collateral Artery (MAPCA) as an isolated congenital anomaly, without evidence of any structural heart disease, is a very rare observation. Previously published reports indicate that symptomatic infants with large isolated MAPCA usually present with congestive heart failure or recurrent respiratory tract infections. To the best of our knowledge, the present case of an infant with large isolated MAPCA is a unique case with a diagnostic dilemma due to presentation with severe pulmonary hypertension as a predominant sign. The infant was managed successfully by percutaneous obliteration with amplatzer vascular plugs, along with perioperative and postoperative sildenafil.
topic amplatzer vascular plug
computed tomography angiogram
sildenafil
url https://jcdr.net/articles/PDF/10094/27645_CE(EK)_F(RK)_PF1(RU_VT_NE)_PFA(PNE).pdf
work_keys_str_mv AT brajeshkumarkunwar largeisolatedmajoraortopulmonarycollateralarterycausingseverepulmonaryhypertensioninaninfantarareandchallengingdiagnosis
AT snigdhapaddalwar largeisolatedmajoraortopulmonarycollateralarterycausingseverepulmonaryhypertensioninaninfantarareandchallengingdiagnosis
AT maheshghogare largeisolatedmajoraortopulmonarycollateralarterycausingseverepulmonaryhypertensioninaninfantarareandchallengingdiagnosis
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