Assessing Function and Endurance in Adults with Spinal and Bulbar Muscular Atrophy: Validity of the Adult Myopathy Assessment Tool

Assessing Function and Endurance in Adults with Spinal and Bulbar Muscular Atrophy: Validity of the Adult Myopathy Assessment Tool

Purpose. The adult myopathy assessment tool (AMAT) is a performance-based battery comprised of functional and endurance subscales that can be completed in approximately 30 minutes without the use of specialized equipment. The purpose of this study was to determine the construct validity and internal...

Full description

Bibliographic Details
Main Authors:	Michael O. Harris-Love, Lindsay Fernandez-Rhodes, Galen Joe, Joseph A. Shrader, Angela Kokkinis, Alison La Pean Kirschner, Sungyoung Auh, Cheunju Chen, Li Li, Ellen Levy, Todd E. Davenport, Nicholas A. Di Prospero, Kenneth H. Fischbeck
Format:	Article
Language:	English
Published:	Hindawi Limited 2014-01-01
Series:	Rehabilitation Research and Practice
Online Access:	http://dx.doi.org/10.1155/2014/873872

Similar Items

Brugada syndrome in spinal and bulbar muscular atrophy
by: 荒木, 周, et al.
Published: (2014)

Stem cell-derived motor neurons from spinal and bulbar muscular atrophy patients
by: Christopher Grunseich, et al.
Published: (2014-10-01)

Acute Thyrotoxic Bulbar Myopathy with Encephalopathic Behaviour: An Uncommon Complication of Hyperthyroidism
by: Neeraja J. Boddu, et al.
Published: (2013-01-01)

Clinical Phenotyping and Biomarkers in Spinal and Bulbar Muscular Atrophy
by: Elina Millere, et al.
Published: (2021-01-01)

Neuropathology and Therapeutic Intervention in Spinal and Bulbar Muscular Atrophy
by: Haruhiko Banno, et al.
Published: (2009-03-01)

Current Status of Treatment of Spinal and Bulbar Muscular Atrophy
by: Fumiaki Tanaka, et al.
Published: (2012-01-01)

Adult-onset bulbar ptosis in Joubert syndrome
by: Burt B, et al.
Published: (2012-01-01)

Spinal and bulbar muscular atrophy (Kennedy’s disease): case description
by: A. V. Gavrichenko, et al.
Published: (2020-02-01)

Proteasomal and autophagic degradative activities in spinal and bulbar muscular atrophy
by: Paola Rusmini, et al.
Published: (2010-11-01)

Rapidly worsening bulbar symptoms in a patient with spinobulbar muscular atrophy
by: Montserrat Diaz-Abad, et al.
Published: (2013-12-01)

Biomarkers of Spinal and Bulbar Muscle Atrophy (SBMA): A Comprehensive Review
by: Giorgia Querin, et al.
Published: (2018-10-01)

Long-term follow-up of spinal and bulbar muscular atrophy in Taiwan
by: Ser-Chen Fu, et al.
Published: (2013-06-01)

Expression of Human Endogenous Retrovirus-K in Spinal and Bulbar Muscular Atrophy
by: Cody Rex, et al.
Published: (2019-09-01)

Genotype-phenotype correlation in Chinese patients with spinal and bulbar muscular atrophy.
by: Wang Ni, et al.
Published: (2015-01-01)

Head and Arm Tremor in X-linked Spinal and Bulbar Muscular Atrophy
by: Irene Aicua, et al.
Published: (2014-10-01)

Assessment of Bulbar Function in Adult Patients with 5q-SMA Type 2 and 3 under Treatment with Nusinersen
by: Svenja Brakemeier, et al.
Published: (2021-09-01)

Olfactory and cortical projections to bulbar and hippocampal adult-born neurons
by: Carlos eDe La Rosa Prieto, et al.
Published: (2015-02-01)

Spinal and bulbar muscular atrophy with pseudomyotonia phenomena: a clinical case report
by: S. S. Nikitin, et al.
Published: (2020-01-01)

Nemo-like kinase is a novel regulator of spinal and bulbar muscular atrophy
by: Tiffany W Todd, et al.
Published: (2015-08-01)

Facial and bulbar muscle atrophy in acetylcholine receptor antibody-positive myasthenia gravis
by: Ronnyson Susano Grativvol, et al.

Tremor in X-linked recessive spinal and bulbar muscular atrophy (Kennedy's disease)
by: Francisco A. Dias, et al.
Published: (2011-01-01)

Recovery of function in a myogenic mouse model of spinal bulbar muscular atrophy
by: Jamie A. Johansen, et al.
Published: (2009-04-01)

Constitutive expression of Yes-associated protein (Yap) in adult skeletal muscle fibres induces muscle atrophy and myopathy.
by: Robert N Judson, et al.
Published: (2013-01-01)

Src inhibition attenuates polyglutamine-mediated neuromuscular degeneration in spinal and bulbar muscular atrophy
by: Madoka Iida, et al.
Published: (2019-09-01)

Enhanced Neural Empathic Responses in Patients with Spino-Bulbar Muscular Atrophy: An Electrophysiological Study
by: Arianna Palmieri, et al.
Published: (2021-12-01)

Change of retrobulbar artery hemodynamics and bulbar conjunctival microcirculation indexes of patients with optic atrophy
by: Dan-Hong Deng
Published: (2015-07-01)

Only some patients with bulbar and spinal muscular atrophy may develop cardiac disease
by: Josef Finsterer, et al.
Published: (2018-03-01)

Factors affecting the aggregation of the androgen receptor protein : implications for spinal and bulbar muscular atrophy
by: Darrington, R. Siobhan
Published: (2003)

Only some patients with bulbar and spinal muscular atrophy may develop cardiac disease
by: Josef Finsterer, et al.
Published: (2018-03-01)

CROSS-SECTIONAL AND LONGITUDINAL ANALYSIS OF AN OXIDATIVE STRESS BIOMARKER FOR SPINAL AND BULBAR MUSCULAR ATROPHY
by: 眞野, 智生, et al.
Published: (2014)

Correlation Between Maximal Tongue Pressure and Swallowing Function in Spinal and Bulbar Muscular Atrophy
by: Dae-Won Gwak, et al.
Published: (2021-09-01)

The pathophysiology of Spinal Bulbar Muscular Atrophy : a longitudinal analysis of muscle and spinal cord
by: Annan, Leonette Victoria Naakuma Delali
Published: (2017)

Neuromuscular junction pathology is correlated with differential motor unit vulnerability in spinal and bulbar muscular atrophy
by: Lieberman, A.P, et al.
Published: (2022)

Novel androgen receptor-protein interactions as possible contributors to the pathogenesis of spinal and bulbar muscular atrophy
by: De Tourreil, Sunita.
Published: (1997)

17-AAG increases autophagic removal of mutant androgen receptor in spinal and bulbar muscular atrophy
by: Paola Rusmini, et al.
Published: (2011-01-01)

GNE Myopathy With Novel Mutations and Pronounced Paraspinal Muscle Atrophy
by: Tyler Soule, et al.
Published: (2018-11-01)

Deterioration of muscle force and contractile characteristics are early pathological events in spinal and bulbar muscular atrophy mice
by: Anna L. Gray, et al.
Published: (2020-05-01)

Human adipose-derived mesenchymal stem cells as a new model of spinal and bulbar muscular atrophy.
by: Marta Dossena, et al.
Published: (2014-01-01)

Autophagic and Proteasomal Mediated Removal of Mutant Androgen Receptor in Muscle Models of Spinal and Bulbar Muscular Atrophy
by: Maria Elena Cicardi, et al.
Published: (2019-08-01)

Peripheral Androgen Receptor Gene Suppression Rescues Disease in Mouse Models of Spinal and Bulbar Muscular Atrophy
by: Andrew P. Lieberman, et al.
Published: (2014-05-01)