Transposition of the great arteries with total anomalous pulmonary venous connection in a 1½year-old child: Pulmonary arterial hypertension - An advantage

• Main Authors: Rose Okwunu Abah, Atul Prabhu, Ashish Katewa, Balswaroop Sahu
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2021-01-01
• Series: Annals of Pediatric Cardiology
• Subjects: anatomic correction; pulmonary arterial hypertension; total anomalous pulmonary venous connection; transposition of the great arteries
• Online Access: http://www.annalspc.com/article.asp?issn=0974-2069;year=2021;volume=14;issue=2;spage=235;epage=238;aulast=Abah

Transposition of the great arteries with total anomalous pulmonary venous connection is a rare anomaly with varied management approach depending on the time of presentation; the management of cases which present early is usually by anatomical surgical approach while late presentation is by physiologic approach. This is due to early left ventricular mass regression as a result of the absence of volume and pressure load to the left ventricle (LV). We report a late presentation (at 1½ years of age) that had a successful anatomic surgical correction because the LV was “prepared” by both pressure and volume load from pulmonary arterial hypertension and large ostium secundum atrial septal defect.