Large aortic aneurysm and dissection in a patient with Marfan's syndrome

• Main Authors: Fernando Pivatto Júnior, Leila Denise Cardoso Ramos, Murilo Foppa, Felipe Soares Torres
• Format: Article
• Language: English
• Published: Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) 2015-04-01
• Series: Clinical and Biomedical Research
• Subjects: Marfan’s syndrome; aortic aneurysm; dissection
• Online Access: http://seer.ufrgs.br/hcpa/article/view/52524
• ISSN: 0101-5575; 2357-9730

Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.