Surgical repair of partial anomalous pulmonary venous return with intact atrial septum in a 65-year-old woman: a case report

• Main Authors: Narihiro Ishida, Katsuya Shimabukuro, Shojiro Yamaguchi, Etsuji Umeda, Hiroki Ogura, Shohei Mitta, Ryutaro Kimata, Hirofumi Takemura, Kiyoshi Doi
• Format: Article
• Language: English
• Published: BMC 2018-11-01
• Series: Journal of Medical Case Reports
• Subjects: Congenital heart disease; Older adult; Cardiac pathology; Pulmonary vein
• Online Access: http://link.springer.com/article/10.1186/s13256-018-1874-x

Abstract Background Partial anomalous pulmonary venous return is a rare congenital cardiac anomaly that usually involves the right pulmonary vein and an atrial septal defect. Isolated partial anomalous pulmonary venous return with an intact atrial septum is even rarer, and this condition is usually treated surgically in younger patients. We describe isolated partial anomalous pulmonary venous return in a 65-year-old woman who was treated by caval division with pericardial patch baffling through a surgically created atrial septal defect and reconstruction of the superior vena cava using a prosthetic graft. Case presentation A 65-year-old Asian woman who presented with exertional dyspnea was diagnosed with isolated partial anomalous pulmonary venous return. The surgical indications and strategy were controversial because of the rarity of this pathology. She had an indication for surgery because she was symptomatic and had a high ratio of pulmonary to systemic blood flow. We considered that surgical procedures should avoid postoperative stenosis of a reconstructed flow tract, sinus node dysfunction, and thrombogenesis. We created a caval division with pericardial patch baffling through a surgically created atrial septal defect and reconstructed the superior vena cava using a prosthetic graft for the isolated partial anomalous pulmonary venous return. She has since remained free of exertional dyspnea, arrhythmia, and thrombotic complications. This surgical strategy is safe and effective for treating isolated partial anomalous pulmonary venous return in older symptomatic adults. Conclusions The long-term outcome of surgical repair of partial anomalous pulmonary venous return with an intact atrial septum in our patient, a symptomatic 65-year-old woman, was excellent.