A case report of variant scimitar syndrome

• Main Authors: Kazem Babazadeh, Hassan Zamani, Hamidreza Ghaemi, Forogh Aliakbarnia omran
• Format: Article
• Language: English
• Published: Babol University of Medical Sciences 2017-09-01
• Series: Caspian Journal of Pediatrics
• Subjects: Scimitar Syndrome; Pulmonary venous; Congenital Abnormality; Right lung hypoplasia; Coarctation aorta
• Online Access: http://caspianjp.ir/browse.php?a_code=A-10-97-1&slc_lang=en&sid=1

Background: Scimitar syndrome (SS) or congenital pulmonary venolobar syndrome is a rare anomaly, most commonly including partial pulmonary venous drainage into the inferior vena cava, right lung hypoplasia, dextroposition of the heart, and anomalous systemic arterial supply from aorta or one of its branches to the right lung. Case report: A 10-day-old female infant was referred to our hospital with systolic murmur and tachypnea. Initial chest x-ray suggested cardiomegaly and displacement of cardiac structures into the right hemithorax, and initial echocardiogram indicated patent ductus arteriosus, coarctation of aorta, atrial septal defect, ventricular septal defect in this infant who was diagnosed as having SS. Conclusions: We can consider Scimitar syndrome for infants with tachypnea, cyanosis, intrauterine growth restriction (IUGR) and right lobe opacity in chest x-ray.