Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress

Generalized lymphangiomatosis (GLA) is a rare lymphatic abnormality, mostly affects children and young individuals and can be a diagnostic challenge because of wide spectrum of clinical manifestations. A 26-year-old woman presented to the emergency department of our institution with respiratory dist...

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Main Authors:	Mersad Mehrnahad, MD, Ali Kord, MD, MPH, Zahra Rezaei, MD, Reza Kord, MD
Format:	Article
Language:	English
Published:	Elsevier 2020-08-01
Series:	Radiology Case Reports
Subjects:	Generalized Lymphangiomatosis Pulmonary lymphangiectasis Lymphatic abnormality Lymphangioma Chylothorax
Online Access:	http://www.sciencedirect.com/science/article/pii/S1930043320301916

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spelling	doaj-60b7d86dd8534faa8e639b248709d3002020-11-25T03:07:24ZengElsevierRadiology Case Reports1930-04332020-08-0115811891193Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distressMersad Mehrnahad, MD0Ali Kord, MD, MPH1Zahra Rezaei, MD2Reza Kord, MD3Department of Radiology, Arak University of Medical Sciences, 1 A'lam-Al-Hoda Street, PO Box (646), Arak 3819693345, Iran; Corresponding author.Division of Interventional Radiology, Department of Diagnostic Radiology, University of Illinois College of Medicine, Chicago, IL, USADepartment of Radiology, Arak University of Medical Sciences, 1 A'lam-Al-Hoda Street, PO Box (646), Arak 3819693345, IranStudent Research Committee, Sari Branch, Islamic Azad University, Sari, IranGeneralized lymphangiomatosis (GLA) is a rare lymphatic abnormality, mostly affects children and young individuals and can be a diagnostic challenge because of wide spectrum of clinical manifestations. A 26-year-old woman presented to the emergency department of our institution with respiratory distress and hypoxia. The patient reported similar episodes for the past 10 years without a definite diagnosis. The imaging study demonstrated findings suggestive of GLA with pulmonary, retroperitoneal and osseous involvements which was confirmed on pathological studies from a lung biopsy. A concise review of the clinical, imaging and pathological findings of GLA is provided in this study. A comprehensive history and physical examination, laboratory and pathological work up and imaging is required to make the diagnosis of GLA. The characteristic imaging findings play an essential role to rule out other possible diagnoses and raise the possibility of GLA.http://www.sciencedirect.com/science/article/pii/S1930043320301916Generalized LymphangiomatosisPulmonary lymphangiectasisLymphatic abnormalityLymphangiomaChylothorax
collection	DOAJ
language	English
format	Article
sources	DOAJ
author	Mersad Mehrnahad, MD Ali Kord, MD, MPH Zahra Rezaei, MD Reza Kord, MD
spellingShingle	Mersad Mehrnahad, MD Ali Kord, MD, MPH Zahra Rezaei, MD Reza Kord, MD Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress Radiology Case Reports Generalized Lymphangiomatosis Pulmonary lymphangiectasis Lymphatic abnormality Lymphangioma Chylothorax
author_facet	Mersad Mehrnahad, MD Ali Kord, MD, MPH Zahra Rezaei, MD Reza Kord, MD
author_sort	Mersad Mehrnahad, MD
title	Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress
title_short	Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress
title_full	Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress
title_fullStr	Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress
title_full_unstemmed	Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress
title_sort	late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress
publisher	Elsevier
series	Radiology Case Reports
issn	1930-0433
publishDate	2020-08-01
description	Generalized lymphangiomatosis (GLA) is a rare lymphatic abnormality, mostly affects children and young individuals and can be a diagnostic challenge because of wide spectrum of clinical manifestations. A 26-year-old woman presented to the emergency department of our institution with respiratory distress and hypoxia. The patient reported similar episodes for the past 10 years without a definite diagnosis. The imaging study demonstrated findings suggestive of GLA with pulmonary, retroperitoneal and osseous involvements which was confirmed on pathological studies from a lung biopsy. A concise review of the clinical, imaging and pathological findings of GLA is provided in this study. A comprehensive history and physical examination, laboratory and pathological work up and imaging is required to make the diagnosis of GLA. The characteristic imaging findings play an essential role to rule out other possible diagnoses and raise the possibility of GLA.
topic	Generalized Lymphangiomatosis Pulmonary lymphangiectasis Lymphatic abnormality Lymphangioma Chylothorax
url	http://www.sciencedirect.com/science/article/pii/S1930043320301916
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Late diagnosis of generalized lymphangiomatosis in a woman presenting with respiratory distress

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