Computed tomography imaging characteristics of shone syndrome

• Main Authors: Alan True, MD, Melvin Baidya, Christopher Lui, MD, German Kilimnik, MD, Michael Sadler, MD
• Format: Article
• Language: English
• Published: Elsevier 2019-02-01
• Series: Radiology Case Reports
• Online Access: http://www.sciencedirect.com/science/article/pii/S1930043318304059
• ISSN: 1930-0433

Shone syndrome was first described in 1963 by Dr JD Shone. It is a constellation of congenital abnormalities compromising approximately 0.6% of all cases of congenital cardiac abnormalities. Shone syndrome is also known as Shone complex, involving several characteristic cardiac abnormalities: coarctation of the aorta, subaortic stenosis, supravalvular mitral ring, and a parachute mitral valve. Given the uncommon nature of the disease, we present this case to illustrate potential postsurgical appearances of Shone syndrome, specifically on computed tomography imaging. Keywords: Shone's, Shone, Congenital, Coarctation, Stenosis, Parachute