A case of Alagille syndrome presenting with chronic cholestasis in an adult
Alagille syndrome (AGS) is a complex multisystem disorder that involves mainly the liver, heart, eyes, face, and skeleton. The main associated clinical features are chronic cholestasis due to a paucity of intrahepatic bile ducts, congenital heart disease primarily affecting pulmonary arteries, verte...
Main Authors: | Jihye Kim, Bumhee Yang, Namyoung Paik, Yon Ho Choe, Yong-Han Paik |
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Format: | Article |
Language: | English |
Published: |
Korean Association for the Study of the Liver
2017-09-01
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Series: | Clinical and Molecular Hepatology |
Subjects: | |
Online Access: | http://e-cmh.org/upload/pdf/cmh-2016-0057.pdf |
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