An unusual cause of urinary incontinence: Urethral coitus in a case of Mayer-Rokitansky-Kuster-Hauser syndrome
Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare anomaly in women and is characterized by congenital aplasia of the uterus and vagina, with normal development of secondary sexual characteristics and a normal karyotype. We report a case of a 38-year-old women with MRKH syndrome that had exp...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Korean Urological Association
2016-09-01
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| Series: | Investigative and Clinical Urology |
| Subjects: | |
| Online Access: | https://www.icurology.org/Synapse/Data/PDFData/2020ICU/icu-57-367.pdf |
| Summary: | Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare anomaly in women and is characterized by congenital aplasia of the
uterus and vagina, with normal development of secondary sexual characteristics and a normal karyotype. We report a case of a
38-year-old women with MRKH syndrome that had experienced urethral sex for many years. She presented with urinary incontinence
and dyspareunia. The patient’s secondary sexual characteristics were normal, and examination revealed a widely open
incompetent megalourethra and an absent vagina. Laboratory studies confirmed a 46, XX karyotype. Imaging included ultrasonography
and magnetic resonance imaging, which indicated bilateral normal ovaries and a rudimental bicornuate uterus. After
confirming the diagnosis of MRKH, the patient underwent urethroplasty by urethral plication, antiincontinence surgery by autologous
fascial sling of the bladder neck, and the creation of a neo-vagina using a urethral flap. After 3 months, voiding cystourethrography
and uroflowmetry confirmed normal voiding. There were no postoperative symptoms of urinary incontinence, and the
patient was completely satisfied.
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| ISSN: | 2466-0493 2466-054X |