Bladder and urethral duplication and a bladder exstrophy plate with omphalocele in a female child

The Exstrophy – Epispadias Complex (EEC) is a spectrum of rare congenital malformations involving the urinary, genital and musculoskeletal systems. We present an atypical or variant case of EEC in which a bladder plate is found involving a small omphalocele, separated pubic bones and bladder and ure...

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Main Authors: Luiz G. Freitas Filho, Ana Carolina Carvalho Fonseca, Taynara Roberta Guerreiro Paiva, Bárbara Stephane de Medeiros Jerônimo, Raphael Miranda Magalhães, Maria Cristina Gomes Abreu, Luiz J. Budib
Format: Article
Language:English
Published: Elsevier 2021-11-01
Series:Urology Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2214442021002096
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Summary:The Exstrophy – Epispadias Complex (EEC) is a spectrum of rare congenital malformations involving the urinary, genital and musculoskeletal systems. We present an atypical or variant case of EEC in which a bladder plate is found involving a small omphalocele, separated pubic bones and bladder and urethral duplication. The treatment had a favorable outcome, with bladder control and the child voiding normally. Perhaps the best accepted embryonic theory to explain exstrophy and its variants should be reviewed as it fails to satisfactorily explain the alterations we found.
ISSN:2214-4420