Soft Tissue Perivascular Epithelioid Cell Tumour: An Unusual Finding

• Main Authors: Mauricio Bermúdez Sagre, Christian Ospina Pérez, Jennyfer Ortega Guatame, Rosa Ospina Perez, Ivan Lozada Martínez, Jennifer Jiménez Valverde, María Bolaño Romero
• Format: Article
• Language: English
• Published: Karolinum Press 2021-06-01
• Series: Prague Medical Report
• Subjects: perivascular epithelioid cell neoplasms; sarcoma; soft tissue neoplasms; rare diseases; case reports
• Online Access: https://pmr.lf1.cuni.cz/122/2/0112/

Perivascular epithelioid cell tumour (PEComa) is a rare mesenchymal tumour made up of clear perivascular cells with epithelioid characteristics, which co-expresses muscle and melanocytic markers with a component of spindle cells, like sarcoma and variety of other tissues. This time, we present the case of a young patient with a tumour in the dorsal region of progressive growth, compatible with PEComa of soft tissue after histopathological and immunohistochemical analysis.