Splenic Kasabach-Merritt syndrome in an adult. Presentation of a case and review of the topic

• Main Authors: Angel Piriz-Momblant, Leuby Portuondo-Bandera, Liudy Luna-Pérez
• Format: Article
• Language: Spanish
• Published: Centro Editorial Ciencias Médicas: CPICM Guantánamo 2021-02-01
• Series: Revista Información Científica
• Subjects: kasabach-merritt; esplenomegalia; hemangioma esplénico; trombocitopenia; coagulopatía de consumo
• Online Access: http://www.revinfcientifica.sld.cu/index.php/ric/article/view/3190

A 22-year-old male black patient presented with big splenomegaly due to a giant hemangioma of the spleen, showing thrombocytopenia and bleeding disorders. A Kasabach-Merrit syndrome was diagnosed. An anterior total splenectomy was performed, returning the platelet count and coagulation disorders back to normal. His evolution was favorable after 18 months of follow-up. Splenectomy surgical treatment was recommended. The topic was reviewed due to the infrequency of the disease.