Gastric outlet obstruction due to neurofibromatosis: An unusual case
Neurofibromatosis type-1 (NF-1), also known as von Recklinghausen disease, is an autosomal dominant condition with an approximate incidence of one in 3000 births. NF-1 is known to involve multiple systems in the body. Abdominal involvement include neurofibroma and tumor growth in the liver, mesenter...
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Format: | Article |
Language: | English |
Published: |
Wolters Kluwer Medknow Publications
2009-01-01
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Series: | The Saudi Journal of Gastroenterology |
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Online Access: | http://www.saudijgastro.com/article.asp?issn=1319-3767;year=2009;volume=15;issue=1;spage=59;epage=61;aulast=Rastogi |
Summary: | Neurofibromatosis type-1 (NF-1), also known as von Recklinghausen disease, is an autosomal dominant condition with an approximate incidence of one in 3000 births. NF-1 is known to involve multiple systems in the body. Abdominal involvement include neurofibroma and tumor growth in the liver, mesentery, and retroperitoneum in addition to gastric and bowel tumors. Gastrointestinal neoplasms occur in up to one quarter of patients. The author reports a rare case of diffuse submucosal neurofibromatosis resulting in gastric outlet obstruction. |
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ISSN: | 1319-3767 1998-4049 |