Idiopathic pleuroparenchymal fibroelastosis: A rare but increasingly recognized entity
Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently described rare entity, characterized by pleural and subpleural parenchymal fibrosis and elastosis mainly in the upper lobes. The etiology and pathophysiology are unknown. The prognosis is poor, with no effective therapies other than l...
| Main Authors: | , , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2015-01-01
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| Series: | Revista Portuguesa de Pneumologia (English Edition) |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2173511514001353 |