An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome

Uterovaginal duplication with imperforated hemivagina is a rare type of Mullerian anomaly. If ipsilateral renal agenesis is associated with this complex genital malformation, it is called Herlyn-Werner-Wunderlich syndrome. Clinical presentations of this syndrome include pelvic pain and mass effect...

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Main Authors: Yasemin Kayadibi, Elmar Bayraktarov, Evrim Özmen, Altay Gezer, İbrahim Adaletli
Format: Article
Language:English
Published: Galenos Yayinevi 2014-03-01
Series:Haseki Tıp Bülteni
Subjects:
Online Access:http://www.hasekidergisi.com/article_4734/An-Unexpected-Cause-Of-Pelvic-Pain-In-A-Pubertal-Case-Herlyn-werner-wunderlich-Syndrome
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spelling doaj-4ad50ff2615241ada09ec0df057239f62020-11-25T01:59:32ZengGalenos YayineviHaseki Tıp Bülteni1302-00722147-26882014-03-01521606310.4274/Haseki.1278An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich SyndromeYasemin Kayadibi0Elmar Bayraktarov1Evrim Özmen2Altay Gezer3İbrahim Adaletli4İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Radyoloji Anabilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Radyoloji Anabilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Radyoloji Anabilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Kadın Hastalıkları ve Doğum Anabilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Radyoloji Anabilim Dalı, İstanbul, Türkiye Uterovaginal duplication with imperforated hemivagina is a rare type of Mullerian anomaly. If ipsilateral renal agenesis is associated with this complex genital malformation, it is called Herlyn-Werner-Wunderlich syndrome. Clinical presentations of this syndrome include pelvic pain and mass effect due to obstructed hemivagina in pubertal adolescents and adults. Hematocolpos, even after menstruation period, leads to misdiagnosis. Laparotomy is the gold standard for the diagnosis, however, magnetic resonance imaging has an accuracy upto 100% in evaluating uterovajinal anatomy. In this article, we aimed to present ultrasonographic and magnetic resonance imaging findings in a patient with Herlyn-Werner-Wun derlich syndrome who presented with cyclic pelvic pain. (The Me­di­cal Bul­le­tin of Ha­se­ki 2014; 52: 60-3)http://www.hasekidergisi.com/article_4734/An-Unexpected-Cause-Of-Pelvic-Pain-In-A-Pubertal-Case-Herlyn-werner-wunderlich-SyndromeHerlyn-Werner-Wunderlichhematocolposmagnetic resonance imagingpelvic painpuberty
collection DOAJ
language English
format Article
sources DOAJ
author Yasemin Kayadibi
Elmar Bayraktarov
Evrim Özmen
Altay Gezer
İbrahim Adaletli
spellingShingle Yasemin Kayadibi
Elmar Bayraktarov
Evrim Özmen
Altay Gezer
İbrahim Adaletli
An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome
Haseki Tıp Bülteni
Herlyn-Werner-Wunderlich
hematocolpos
magnetic resonance imaging
pelvic pain
puberty
author_facet Yasemin Kayadibi
Elmar Bayraktarov
Evrim Özmen
Altay Gezer
İbrahim Adaletli
author_sort Yasemin Kayadibi
title An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome
title_short An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome
title_full An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome
title_fullStr An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome
title_full_unstemmed An Unexpected Cause of Pelvic Pain in a Pubertal Case: Herlyn-Werner-Wunderlich Syndrome
title_sort unexpected cause of pelvic pain in a pubertal case: herlyn-werner-wunderlich syndrome
publisher Galenos Yayinevi
series Haseki Tıp Bülteni
issn 1302-0072
2147-2688
publishDate 2014-03-01
description Uterovaginal duplication with imperforated hemivagina is a rare type of Mullerian anomaly. If ipsilateral renal agenesis is associated with this complex genital malformation, it is called Herlyn-Werner-Wunderlich syndrome. Clinical presentations of this syndrome include pelvic pain and mass effect due to obstructed hemivagina in pubertal adolescents and adults. Hematocolpos, even after menstruation period, leads to misdiagnosis. Laparotomy is the gold standard for the diagnosis, however, magnetic resonance imaging has an accuracy upto 100% in evaluating uterovajinal anatomy. In this article, we aimed to present ultrasonographic and magnetic resonance imaging findings in a patient with Herlyn-Werner-Wun derlich syndrome who presented with cyclic pelvic pain. (The Me­di­cal Bul­le­tin of Ha­se­ki 2014; 52: 60-3)
topic Herlyn-Werner-Wunderlich
hematocolpos
magnetic resonance imaging
pelvic pain
puberty
url http://www.hasekidergisi.com/article_4734/An-Unexpected-Cause-Of-Pelvic-Pain-In-A-Pubertal-Case-Herlyn-werner-wunderlich-Syndrome
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