Discinesia ciliar primária: considerações sobre seis casos da síndrome de Kartagener Primary ciliary dyskinesia: considerations regarding six cases of Kartagener syndrome

Discinesia ciliar primária: considerações sobre seis casos da síndrome de Kartagener Primary ciliary dyskinesia: considerations regarding six cases of Kartagener syndrome

A discinesia ciliar primária (DCP), anteriormente conhecida como síndrome dos cílios imóveis, é uma doença hereditária autossômica recessiva que inclui vários padrões de defeitos em sua ultra-estrutura ciliar. Sua forma clínica mais grave é a síndrome de Kartagener (SK), a qual é encontrada em 50% d...

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Bibliographic Details
Main Authors:	Hugo Alejandro Vega Ortega, Nelson de Araujo Vega, Bruno Quirino dos Santos, Guilherme Tavares da Silva Maia
Format:	Article
Language:	English
Published:	Sociedade Brasileira de Pneumologia e Tisiologia 2007-10-01
Series:	Jornal Brasileiro de Pneumologia
Subjects:	Síndrome de Kartagener Transtornos da motilidade ciliar Bronquiectasia Dextrocardia Kartagener syndrome Ciliary motility disorders Bronchiectasis
Online Access:	http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132007000500017

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