Skeletal Dysplasias Caused by Sulfation Defects

Skeletal Dysplasias Caused by Sulfation Defects

Proteoglycans (PGs) are macromolecules present on the cell surface and in the extracellular matrix that confer specific mechanical, biochemical, and physical properties to tissues. Sulfate groups present on glycosaminoglycans, linear polysaccharide chains attached to PG core proteins, are fundamenta...

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Bibliographic Details
Main Authors:	Chiara Paganini, Chiara Gramegna Tota, Andrea Superti-Furga, Antonio Rossi
Format:	Article
Language:	English
Published:	MDPI AG 2020-04-01
Series:	International Journal of Molecular Sciences
Subjects:	sulfate metabolism sulfotransferase glycosaminoglycan proteoglycan cartilage genotype phenotype correlation
Online Access:	https://www.mdpi.com/1422-0067/21/8/2710

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