Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)

Herlyn–Werner–Wunderlich syndrome (OHVIRA syndrome) is a combined malformation of the genitourinary systeme, characterized by various combinations of uterus dydelphys with unilateral obstructed (or blind) hemivagina and ipsilateral renal agenesis. The causes of mistakes in diagnosis and treatment ar...

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Main Authors: K. Kh. Alieva, N. A. Kokhreidze, A. A. Sukhotskaya, V. G. Bairov, A. Yu. Skripnik
Format: Article
Language:Russian
Published: ABV-press 2021-02-01
Series:Andrologiâ i Genitalʹnaâ Hirurgiâ
Subjects:
Online Access:https://agx.abvpress.ru/jour/article/view/459
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spelling doaj-3c1b0913ef06416985e6fd195408537c2021-07-29T09:03:56ZrusABV-pressAndrologiâ i Genitalʹnaâ Hirurgiâ2070-97812021-02-01214606710.17650/2070-9781-2020-21-4-60-67388Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)K. Kh. Alieva0N. A. Kokhreidze1A. A. Sukhotskaya2V. G. Bairov3A. Yu. Skripnik4V. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaHerlyn–Werner–Wunderlich syndrome (OHVIRA syndrome) is a combined malformation of the genitourinary systeme, characterized by various combinations of uterus dydelphys with unilateral obstructed (or blind) hemivagina and ipsilateral renal agenesis. The causes of mistakes in diagnosis and treatment are common because of relative rarity of anomaly, insufficient awareness of practitioners about the syndrome and the lack of multidisciplinary approach. Untimely and tactically chaotic diagnosis of Herlyn–Werner–Wunderlich syndrome leads to a misconception about the clinical situation, wrong choice in treatment, and, as a consequence, to complications such as strictures, widespread adhesions and inflammation, as well as irreversible changes in the topography of organs of the small pelvis with a subsequent deterioration in reproductive status of patient. This article provides a review of the literature on the problem, considers the clinical cases of diagnosing this defect in prepubertal patients.https://agx.abvpress.ru/jour/article/view/459ohvira syndromeherlyn–werner–wunderlich syndromepyocolposrenal agenesis
collection DOAJ
language Russian
format Article
sources DOAJ
author K. Kh. Alieva
N. A. Kokhreidze
A. A. Sukhotskaya
V. G. Bairov
A. Yu. Skripnik
spellingShingle K. Kh. Alieva
N. A. Kokhreidze
A. A. Sukhotskaya
V. G. Bairov
A. Yu. Skripnik
Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
Andrologiâ i Genitalʹnaâ Hirurgiâ
ohvira syndrome
herlyn–werner–wunderlich syndrome
pyocolpos
renal agenesis
author_facet K. Kh. Alieva
N. A. Kokhreidze
A. A. Sukhotskaya
V. G. Bairov
A. Yu. Skripnik
author_sort K. Kh. Alieva
title Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
title_short Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
title_full Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
title_fullStr Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
title_full_unstemmed Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
title_sort herlyn–werner–wunderlich syndrome in the prepubescent period (literature review and clinical observations)
publisher ABV-press
series Andrologiâ i Genitalʹnaâ Hirurgiâ
issn 2070-9781
publishDate 2021-02-01
description Herlyn–Werner–Wunderlich syndrome (OHVIRA syndrome) is a combined malformation of the genitourinary systeme, characterized by various combinations of uterus dydelphys with unilateral obstructed (or blind) hemivagina and ipsilateral renal agenesis. The causes of mistakes in diagnosis and treatment are common because of relative rarity of anomaly, insufficient awareness of practitioners about the syndrome and the lack of multidisciplinary approach. Untimely and tactically chaotic diagnosis of Herlyn–Werner–Wunderlich syndrome leads to a misconception about the clinical situation, wrong choice in treatment, and, as a consequence, to complications such as strictures, widespread adhesions and inflammation, as well as irreversible changes in the topography of organs of the small pelvis with a subsequent deterioration in reproductive status of patient. This article provides a review of the literature on the problem, considers the clinical cases of diagnosing this defect in prepubertal patients.
topic ohvira syndrome
herlyn–werner–wunderlich syndrome
pyocolpos
renal agenesis
url https://agx.abvpress.ru/jour/article/view/459
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AT aasukhotskaya herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations
AT vgbairov herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations
AT ayuskripnik herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations
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