Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)
Herlyn–Werner–Wunderlich syndrome (OHVIRA syndrome) is a combined malformation of the genitourinary systeme, characterized by various combinations of uterus dydelphys with unilateral obstructed (or blind) hemivagina and ipsilateral renal agenesis. The causes of mistakes in diagnosis and treatment ar...
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Series: | Andrologiâ i Genitalʹnaâ Hirurgiâ |
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Online Access: | https://agx.abvpress.ru/jour/article/view/459 |
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doaj-3c1b0913ef06416985e6fd195408537c2021-07-29T09:03:56ZrusABV-pressAndrologiâ i Genitalʹnaâ Hirurgiâ2070-97812021-02-01214606710.17650/2070-9781-2020-21-4-60-67388Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations)K. Kh. Alieva0N. A. Kokhreidze1A. A. Sukhotskaya2V. G. Bairov3A. Yu. Skripnik4V. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaV. A. Almazov National Medical Research Center, Ministry of Health of RussiaHerlyn–Werner–Wunderlich syndrome (OHVIRA syndrome) is a combined malformation of the genitourinary systeme, characterized by various combinations of uterus dydelphys with unilateral obstructed (or blind) hemivagina and ipsilateral renal agenesis. The causes of mistakes in diagnosis and treatment are common because of relative rarity of anomaly, insufficient awareness of practitioners about the syndrome and the lack of multidisciplinary approach. Untimely and tactically chaotic diagnosis of Herlyn–Werner–Wunderlich syndrome leads to a misconception about the clinical situation, wrong choice in treatment, and, as a consequence, to complications such as strictures, widespread adhesions and inflammation, as well as irreversible changes in the topography of organs of the small pelvis with a subsequent deterioration in reproductive status of patient. This article provides a review of the literature on the problem, considers the clinical cases of diagnosing this defect in prepubertal patients.https://agx.abvpress.ru/jour/article/view/459ohvira syndromeherlyn–werner–wunderlich syndromepyocolposrenal agenesis |
collection |
DOAJ |
language |
Russian |
format |
Article |
sources |
DOAJ |
author |
K. Kh. Alieva N. A. Kokhreidze A. A. Sukhotskaya V. G. Bairov A. Yu. Skripnik |
spellingShingle |
K. Kh. Alieva N. A. Kokhreidze A. A. Sukhotskaya V. G. Bairov A. Yu. Skripnik Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations) Andrologiâ i Genitalʹnaâ Hirurgiâ ohvira syndrome herlyn–werner–wunderlich syndrome pyocolpos renal agenesis |
author_facet |
K. Kh. Alieva N. A. Kokhreidze A. A. Sukhotskaya V. G. Bairov A. Yu. Skripnik |
author_sort |
K. Kh. Alieva |
title |
Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations) |
title_short |
Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations) |
title_full |
Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations) |
title_fullStr |
Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations) |
title_full_unstemmed |
Herlyn–Werner–Wunderlich syndrome in the prepubescent period (literature review and clinical observations) |
title_sort |
herlyn–werner–wunderlich syndrome in the prepubescent period (literature review and clinical observations) |
publisher |
ABV-press |
series |
Andrologiâ i Genitalʹnaâ Hirurgiâ |
issn |
2070-9781 |
publishDate |
2021-02-01 |
description |
Herlyn–Werner–Wunderlich syndrome (OHVIRA syndrome) is a combined malformation of the genitourinary systeme, characterized by various combinations of uterus dydelphys with unilateral obstructed (or blind) hemivagina and ipsilateral renal agenesis. The causes of mistakes in diagnosis and treatment are common because of relative rarity of anomaly, insufficient awareness of practitioners about the syndrome and the lack of multidisciplinary approach. Untimely and tactically chaotic diagnosis of Herlyn–Werner–Wunderlich syndrome leads to a misconception about the clinical situation, wrong choice in treatment, and, as a consequence, to complications such as strictures, widespread adhesions and inflammation, as well as irreversible changes in the topography of organs of the small pelvis with a subsequent deterioration in reproductive status of patient. This article provides a review of the literature on the problem, considers the clinical cases of diagnosing this defect in prepubertal patients. |
topic |
ohvira syndrome herlyn–werner–wunderlich syndrome pyocolpos renal agenesis |
url |
https://agx.abvpress.ru/jour/article/view/459 |
work_keys_str_mv |
AT kkhalieva herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations AT nakokhreidze herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations AT aasukhotskaya herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations AT vgbairov herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations AT ayuskripnik herlynwernerwunderlichsyndromeintheprepubescentperiodliteraturereviewandclinicalobservations |
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