Williams–Campbell Syndrome: A Rare Differential of Cystic Bronchiectasis

• Main Authors: Tanvi Meha, Anshul Raja, Anil Kumar Jaiswal
• Format: Article
• Language: English
• Published: ADICHUNCHANAGIRI INSTITUTE OF MEDICAL SCIENCES 2016-10-01
• Series: Journal of Medical Sciences and Health
• Subjects: pancreatitis; alcoholic; amylases; lipase; bilirubin
• Online Access: http://www.jmsh.ac.in/index.php?option=com_k2&view=item&id=64:williams%E2%80%93campbell-syndrome-a-rare-differential-of-cystic-bronchiectasis&Itemid=76

Williams–Campbell syndrome is a rare congenital syndrome characterized by the absence of cartilage in subsegmental bronchi leading to formation of bronchiectasis distal to the affected bronchi. The syndrome is usually presented in childhood, with recurrent pneumonia and broncho-obstructive symptoms such as coughing and wheezing. When patients’ signs and symptoms include recurrent respiratory infections and diffuse bronchiectasis, Williams–Campbell syndrome should be included in the differential diagnosis. The authors hereby report a case of a 1.5-year-old male child with respiratory distress who was diagnosed as Williams–Campbell syndrome on clinico-radiological grounds.