Primary Intestinal Lymphangiectasia (Waldmann’s Disease) Presenting with Chylous Effusions in a 15-Year-Old

Primary Intestinal Lymphangiectasia (PIL) is a rare disease of unknown aetiology which presents in the paediatric age group with anasarca, diarrhoea, hypoproteinaemia, lymphoedema and chylous effusions. Tuberculosis, filariasis, chest trauma, malignancies and haematological disorders usually contr...

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Bibliographic Details
Main Authors: Vijay Surampalli, Srinath Ramaswamy, Deepanjali Surendran, Chanaveerappa Bammigatti, Rathinam Palamalai Swaminathan
Format: Article
Language:English
Published: JCDR Research and Publications Private Limited 2017-08-01
Series:Journal of Clinical and Diagnostic Research
Subjects:
Online Access:https://jcdr.net/articles/PDF/10522/29055_CE[Ra]_F(Sh)_PF1(VT_GG)_PFA(VT_GG).pdf
Description
Summary:Primary Intestinal Lymphangiectasia (PIL) is a rare disease of unknown aetiology which presents in the paediatric age group with anasarca, diarrhoea, hypoproteinaemia, lymphoedema and chylous effusions. Tuberculosis, filariasis, chest trauma, malignancies and haematological disorders usually contribute to most cases of secondary lymphangiectasia and chylous effusions. We hereby describe a case of PIL presenting with chylous effusions which remained undiagnosed for eight years.
ISSN:2249-782X
0973-709X