Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder

ntroduction: Reduced intrauterine space gives rise to ‘packaging disorder’ which may involve joint dislocations or contractures. We present an unique case where mutiple joints were dislocated involving left congenital knee dislocation (CDK), bilateral congenital hip dislocation (CDH) and congenital...

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Main Authors: Mukesh Tiwari, Nishith Sharma
Format: Article
Language:English
Published: Indian Orthopaedic Research Group 2013-04-01
Series:Journal of Orthopaedic Case Reports
Online Access:http://www.jocr.co.in/wp/2013/04/13/2250-0685-096-fulltext/
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spelling doaj-3357a1e5edbc463ea840b71a584bf11b2020-11-25T02:44:08ZengIndian Orthopaedic Research GroupJournal of Orthopaedic Case Reports2250-06852013-04-0132212410.13107/jocr.2250-0685.096 Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorderMukesh Tiwari0Nishith Sharma1NIMS Medical College, Jaipur. Rajasthan, IndiaNIMS Medical College, Jaipur. Rajasthan, Indiantroduction: Reduced intrauterine space gives rise to ‘packaging disorder’ which may involve joint dislocations or contractures. We present an unique case where mutiple joints were dislocated involving left congenital knee dislocation (CDK), bilateral congenital hip dislocation (CDH) and congenital talipes equino varus (CTEV)deformities. Case Report: A preterm baby boy born to mother with diagnosed oligohydramios presented with left CDK bilateral DDH and CTEV. The knee dislocation was treated first with gradual streaching and weekly above knee cast. At 7th week good flexion was achieved at both knees and abduction splint for DDH (using double diaper) with ponseti cast for CTEV was done. At one year follow up all joints were reduced and maintained well with baby able to stand with support. Conclusion: Packaging disorders may present with multiple dislocations and deformities. Early intervention with serial casting and manipulation minimises disability and prevents ambulatory problems. In our case there was a good response to manipulation and serial casting. This differs from cases with inherent pathology like arthrogryposis where response to treatment is not so good. Keywords: Congenital genu recurvatum, Develpmental dysplasia hip, CTEV, Clubfoot, serial manipulation, packaging disordershttp://www.jocr.co.in/wp/2013/04/13/2250-0685-096-fulltext/
collection DOAJ
language English
format Article
sources DOAJ
author Mukesh Tiwari
Nishith Sharma
spellingShingle Mukesh Tiwari
Nishith Sharma
Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
Journal of Orthopaedic Case Reports
author_facet Mukesh Tiwari
Nishith Sharma
author_sort Mukesh Tiwari
title Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
title_short Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
title_full Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
title_fullStr Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
title_full_unstemmed Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
title_sort unilateral congenital knee and hip dislocation with bilateral clubfoot – a rare packaging disorder
publisher Indian Orthopaedic Research Group
series Journal of Orthopaedic Case Reports
issn 2250-0685
publishDate 2013-04-01
description ntroduction: Reduced intrauterine space gives rise to ‘packaging disorder’ which may involve joint dislocations or contractures. We present an unique case where mutiple joints were dislocated involving left congenital knee dislocation (CDK), bilateral congenital hip dislocation (CDH) and congenital talipes equino varus (CTEV)deformities. Case Report: A preterm baby boy born to mother with diagnosed oligohydramios presented with left CDK bilateral DDH and CTEV. The knee dislocation was treated first with gradual streaching and weekly above knee cast. At 7th week good flexion was achieved at both knees and abduction splint for DDH (using double diaper) with ponseti cast for CTEV was done. At one year follow up all joints were reduced and maintained well with baby able to stand with support. Conclusion: Packaging disorders may present with multiple dislocations and deformities. Early intervention with serial casting and manipulation minimises disability and prevents ambulatory problems. In our case there was a good response to manipulation and serial casting. This differs from cases with inherent pathology like arthrogryposis where response to treatment is not so good. Keywords: Congenital genu recurvatum, Develpmental dysplasia hip, CTEV, Clubfoot, serial manipulation, packaging disorders
url http://www.jocr.co.in/wp/2013/04/13/2250-0685-096-fulltext/
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