Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder
ntroduction: Reduced intrauterine space gives rise to ‘packaging disorder’ which may involve joint dislocations or contractures. We present an unique case where mutiple joints were dislocated involving left congenital knee dislocation (CDK), bilateral congenital hip dislocation (CDH) and congenital...
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Indian Orthopaedic Research Group
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doaj-3357a1e5edbc463ea840b71a584bf11b2020-11-25T02:44:08ZengIndian Orthopaedic Research GroupJournal of Orthopaedic Case Reports2250-06852013-04-0132212410.13107/jocr.2250-0685.096 Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorderMukesh Tiwari0Nishith Sharma1NIMS Medical College, Jaipur. Rajasthan, IndiaNIMS Medical College, Jaipur. Rajasthan, Indiantroduction: Reduced intrauterine space gives rise to ‘packaging disorder’ which may involve joint dislocations or contractures. We present an unique case where mutiple joints were dislocated involving left congenital knee dislocation (CDK), bilateral congenital hip dislocation (CDH) and congenital talipes equino varus (CTEV)deformities. Case Report: A preterm baby boy born to mother with diagnosed oligohydramios presented with left CDK bilateral DDH and CTEV. The knee dislocation was treated first with gradual streaching and weekly above knee cast. At 7th week good flexion was achieved at both knees and abduction splint for DDH (using double diaper) with ponseti cast for CTEV was done. At one year follow up all joints were reduced and maintained well with baby able to stand with support. Conclusion: Packaging disorders may present with multiple dislocations and deformities. Early intervention with serial casting and manipulation minimises disability and prevents ambulatory problems. In our case there was a good response to manipulation and serial casting. This differs from cases with inherent pathology like arthrogryposis where response to treatment is not so good. Keywords: Congenital genu recurvatum, Develpmental dysplasia hip, CTEV, Clubfoot, serial manipulation, packaging disordershttp://www.jocr.co.in/wp/2013/04/13/2250-0685-096-fulltext/ |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Mukesh Tiwari Nishith Sharma |
spellingShingle |
Mukesh Tiwari Nishith Sharma Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder Journal of Orthopaedic Case Reports |
author_facet |
Mukesh Tiwari Nishith Sharma |
author_sort |
Mukesh Tiwari |
title |
Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder |
title_short |
Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder |
title_full |
Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder |
title_fullStr |
Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder |
title_full_unstemmed |
Unilateral Congenital Knee and Hip Dislocation with Bilateral Clubfoot – A rare Packaging disorder |
title_sort |
unilateral congenital knee and hip dislocation with bilateral clubfoot – a rare packaging disorder |
publisher |
Indian Orthopaedic Research Group |
series |
Journal of Orthopaedic Case Reports |
issn |
2250-0685 |
publishDate |
2013-04-01 |
description |
ntroduction: Reduced intrauterine space gives rise to ‘packaging disorder’ which may involve joint dislocations or contractures. We present an unique case where mutiple joints were dislocated involving left congenital knee dislocation (CDK), bilateral congenital hip dislocation (CDH) and congenital talipes equino varus (CTEV)deformities.
Case Report: A preterm baby boy born to mother with diagnosed oligohydramios presented with left CDK bilateral DDH and CTEV. The knee dislocation was treated first with gradual streaching and weekly above knee cast. At 7th week good flexion was achieved at both knees and abduction splint for DDH (using double diaper) with ponseti cast for CTEV was done. At one year follow up all joints were reduced and maintained well with baby able to stand with support.
Conclusion: Packaging disorders may present with multiple dislocations and deformities. Early intervention with serial casting and manipulation minimises disability and prevents ambulatory problems. In our case there was a good response to manipulation and serial casting. This differs from cases with inherent pathology like arthrogryposis where response to treatment is not so good.
Keywords: Congenital genu recurvatum, Develpmental dysplasia hip, CTEV, Clubfoot, serial manipulation, packaging disorders |
url |
http://www.jocr.co.in/wp/2013/04/13/2250-0685-096-fulltext/ |
work_keys_str_mv |
AT mukeshtiwari unilateralcongenitalkneeandhipdislocationwithbilateralclubfootararepackagingdisorder AT nishithsharma unilateralcongenitalkneeandhipdislocationwithbilateralclubfootararepackagingdisorder |
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