Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases

Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases

Hepatic angiomyolipoma is an extremely rare benign hamartomatous lesion. Situs inversus totalis is a genetic condition occurring in 0.01% of the population. Following the kidney, the liver is the second most common site of angiomyolipoma. No consensus on the treatment of hepatic angiomyolipoma has b...

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Main Authors: Jonathan Mayes, Nigel Heaton
Format: Article
Language:English
Published: Hindawi Limited 2016-01-01
Series:Case Reports in Hepatology
Online Access:http://dx.doi.org/10.1155/2016/5060284
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spelling doaj-2d3ba325d7f840ddab9ee406cfb501b72020-11-24T22:34:26ZengHindawi LimitedCase Reports in Hepatology2090-65872090-65952016-01-01201610.1155/2016/50602845060284Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare DiseasesJonathan Mayes0Nigel Heaton1Newcastle University, Newcastle upon Tyne NE1 7RU, UKInstitute of Liver Studies, King’s Health Partners, King’s College Hospital NHS FT, Denmark Hill, Camberwell, London SE5 9RS, UKHepatic angiomyolipoma is an extremely rare benign hamartomatous lesion. Situs inversus totalis is a genetic condition occurring in 0.01% of the population. Following the kidney, the liver is the second most common site of angiomyolipoma. No consensus on the treatment of hepatic angiomyolipoma has been reached. However, the majority of these tumours are managed conservatively. Situs inversus totalis presents difficulties for procedures and is most commonly an incidental finding. These two conditions have not previously been reported and no genetic link has been established between them. This paper reports the association of both conditions in a 74-year-old female, reviews the literature, and presents CT imaging of the case.http://dx.doi.org/10.1155/2016/5060284
collection DOAJ
language English
format Article
sources DOAJ
author Jonathan Mayes
Nigel Heaton
spellingShingle Jonathan Mayes
Nigel Heaton
Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
Case Reports in Hepatology
author_facet Jonathan Mayes
Nigel Heaton
author_sort Jonathan Mayes
title Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
title_short Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
title_full Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
title_fullStr Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
title_full_unstemmed Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
title_sort angiomyolipoma in a patient with situs inversus totalis: managing two rare diseases
publisher Hindawi Limited
series Case Reports in Hepatology
issn 2090-6587
2090-6595
publishDate 2016-01-01
description Hepatic angiomyolipoma is an extremely rare benign hamartomatous lesion. Situs inversus totalis is a genetic condition occurring in 0.01% of the population. Following the kidney, the liver is the second most common site of angiomyolipoma. No consensus on the treatment of hepatic angiomyolipoma has been reached. However, the majority of these tumours are managed conservatively. Situs inversus totalis presents difficulties for procedures and is most commonly an incidental finding. These two conditions have not previously been reported and no genetic link has been established between them. This paper reports the association of both conditions in a 74-year-old female, reviews the literature, and presents CT imaging of the case.
url http://dx.doi.org/10.1155/2016/5060284
work_keys_str_mv AT jonathanmayes angiomyolipomainapatientwithsitusinversustotalismanagingtworarediseases
AT nigelheaton angiomyolipomainapatientwithsitusinversustotalismanagingtworarediseases
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