Delayed appearance of mature ganglia in an infant with an atypical presentation of total colonic and small bowel aganglionosis: a case report

Delayed appearance of mature ganglia in an infant with an atypical presentation of total colonic and small bowel aganglionosis: a case report

Abstract Background Total colonic and small bowel aganglionosis (TCSA) occurs in less than 1% of all Hirschsprung’s disease patients. Currently, the mainstay of treatment is surgery. However, in patients with TCSA, functional outcomes are often poor. A characteristic transition zone in TCSA can be d...

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Bibliographic Details
Main Authors: Fereshteh Salimi Jazi, Julia M. Chandler, Chad M. Thorson, Tiffany J. Sinclair, Florette K. Hazard, John A. Kerner, Sanjeev Dutta, James C.Y. Dunn, Stephanie D. Chao
Format: Article
Language:English
Published: BMC 2019-04-01
Series:BMC Pediatrics
Subjects:
Aganglionosis
Hirschsprung’s disease
Total colonic aganglionosis
Total colonic and small bowel aganglionosis
Online Access:http://link.springer.com/article/10.1186/s12887-019-1456-0

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