Concomitant pancreatic neuroendocrine tumors in hereditary tumor syndromes: who, when and how to operate?

Abstract. Pancreatic neuroendocrine tumors (pNETs) might present as part of a complex of hereditary (familial) syndromes caused by germline mutations such as multiple endocrine neoplasia type 1 (MEN1), von Hippel–Lindau syndrome (VHL), tuberous sclerosis, and neurofibromatosis syndromes. Hereditary...

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Bibliographic Details
Main Authors: Xu Han, PhD, MD, Wenhui Lou, PhD, MD
Format: Article
Language:English
Published: Wolters Kluwer Health/LWW 2019-06-01
Series:Journal of Pancreatology
Online Access:http://journals.lww.com/10.1097/JP9.0000000000000016