Cystic hemispheric medulloepithelioma

Medulloepithelioma is a rare primitive embryonal tumour of the central nervous system which typically occurs in early childhood. The histopathological appearance has been confused with primitive neuroectodermal tumours (PNETs), but medulloepitheliomas have a more aggressive clinical course. Imaging...

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Bibliographic Details
Main Authors: Jacqueline du Toit, Tracy Kilborn, Llewellyn Padayachy, Komala Pillay, Marc Hendricks
Format: Article
Language:English
Published: AOSIS 2015-12-01
Series:South African Journal of Radiology
Online Access:https://sajr.org.za/index.php/sajr/article/view/915
Description
Summary:Medulloepithelioma is a rare primitive embryonal tumour of the central nervous system which typically occurs in early childhood. The histopathological appearance has been confused with primitive neuroectodermal tumours (PNETs), but medulloepitheliomas have a more aggressive clinical course. Imaging typically demonstrates a well-circumscribed, poorly or non-enhancing solid mass, with cyst formation being infrequent. We report the imaging findings in a case of a cystic hemispheric medulloepithelioma. The importance of considering this diagnosis is discussed in view of the propensity to aggressive recurrence in subtotal resection.
ISSN:1027-202X
2078-6778