Corkscrew aortic arch in PHACES syndrome: Multimodal imaging of an unusual morphology of tortuous aortic arch in a rare but well-defined syndrome

Corkscrew aortic arch in PHACES syndrome: Multimodal imaging of an unusual morphology of tortuous aortic arch in a rare but well-defined syndrome

PHACES syndrome, a diffuse aortocraniocerebral vasculopathy, is a neural tube migration disorder, characterized by aortic coarctation and aberrant arch branches. Clinical diagnosis, echocardiography, and surgical management of coarctation in this syndrome are challenging due to peculiar morphologica...

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Bibliographic Details
Main Authors: Ronak Sheth, Arvind Sahay Singh, Sreeja Pavithran, Kothandam Sivakumar
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2019-01-01
Series:Annals of Pediatric Cardiology
Subjects:
Aortic arch anomaly
corkscrew aorta
hemangioma
neural crest disorder
PHACES syndrome
tortuous aorta
Online Access:http://www.annalspc.com/article.asp?issn=0974-2069;year=2019;volume=12;issue=3;spage=333;epage=335;aulast=

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