Characteristics of lipid metabolism and the cardiovascular system in glycogenosis types I and III

Characteristics of lipid metabolism and the cardiovascular system in glycogenosis types I and III

Glycogen storage disease (GSD) is an inherited metabolic disorder characterized by early childhood lipid metabolic disturbances with potentially proatherogenic effects. The review outlines the characteristics of impaired lipid composition and other changes in the cardiovascular system in GSD types I...

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Bibliographic Details
Main Authors:	N V Polenova, T V Strokova, A V Starodubova
Format:	Article
Language:	Russian
Published:	"Consilium Medicum" Publishing house 2017-08-01
Series:	Терапевтический архив
Subjects:	glycogen storage disease dyslipidemia subclinical atherosclerosis rare (orphan) diseases lipid paradox
Online Access:	https://ter-arkhiv.ru/0040-3660/article/viewFile/32324/pdf

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