Multiple pterygium syndrome: Challenge for anesthesiologist

Multiple pterygium syndrome: Challenge for anesthesiologist

Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of t...

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Bibliographic Details
Main Authors: P Sethi, P K Bhatia, N Gupta, K Singh
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2016-01-01
Series:Saudi Journal of Anaesthesia
Subjects:
Anesthesia; challenges; multiple pterygium syndrome
Online Access:http://www.saudija.org/article.asp?issn=1658-354X;year=2016;volume=10;issue=3;spage=350;epage=352;aulast=Sethi
Description
Summary:Multiple pterygium syndrome (MPS) is a very rare autosomal recessive disorder characterized by flexion of joint and digit contractures, skin webbing, cleft palate, deformity of the spine, and cervical spine fusion. Difficult airway is associated mainly due to micrognathia, retrognathia, webbing of the neck, and limitation of the mouth opening and neck extension. We are reporting a case of a 5-year-old female diagnosed with MPS and exhibiting a bilateral club foot and congenital vertical talus. The patient was posted for manipulation and above the knee casting under general anesthesia.
ISSN:1658-354X

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